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Parachute mitral valve and Pacman deformity of the ventricular septum in a middle-aged male
Parachute mitral valve and Pacman heart (incomplete muscular ventricular septal defect) are rare congenital deformities usually reported in infants and children. Very few adult patients with these anomalies are reported but the association of the two has not been described. This report describes a 5...
Autores principales: | , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Elsevier
2016
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5067460/ https://www.ncbi.nlm.nih.gov/pubmed/27751263 http://dx.doi.org/10.1016/j.ihj.2015.09.012 |
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author | Mohan, Jagdish C. Shukla, Madhu Mohan, Vishwas Sethi, Arvind |
author_facet | Mohan, Jagdish C. Shukla, Madhu Mohan, Vishwas Sethi, Arvind |
author_sort | Mohan, Jagdish C. |
collection | PubMed |
description | Parachute mitral valve and Pacman heart (incomplete muscular ventricular septal defect) are rare congenital deformities usually reported in infants and children. Very few adult patients with these anomalies are reported but the association of the two has not been described. This report describes a 56-year-old male with exertional dyspnea who was detected to have moderately severe mitral regurgitation and mitral stenosis. Typical parachute deformity of the mitral valve with a reduced opening and common attachment of all the chordae to a single posteromedial papillary muscle was evident. The chordae were elongated, lax, and redundant, which is atypical for this anomaly. Incidentally, detected aneurysm of the basal muscular interventricular septum (Pacman deformity or incomplete triangular septal defect) was also present. |
format | Online Article Text |
id | pubmed-5067460 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2016 |
publisher | Elsevier |
record_format | MEDLINE/PubMed |
spelling | pubmed-50674602017-09-01 Parachute mitral valve and Pacman deformity of the ventricular septum in a middle-aged male Mohan, Jagdish C. Shukla, Madhu Mohan, Vishwas Sethi, Arvind Indian Heart J Case Reports Parachute mitral valve and Pacman heart (incomplete muscular ventricular septal defect) are rare congenital deformities usually reported in infants and children. Very few adult patients with these anomalies are reported but the association of the two has not been described. This report describes a 56-year-old male with exertional dyspnea who was detected to have moderately severe mitral regurgitation and mitral stenosis. Typical parachute deformity of the mitral valve with a reduced opening and common attachment of all the chordae to a single posteromedial papillary muscle was evident. The chordae were elongated, lax, and redundant, which is atypical for this anomaly. Incidentally, detected aneurysm of the basal muscular interventricular septum (Pacman deformity or incomplete triangular septal defect) was also present. Elsevier 2016-09 2015-12-22 /pmc/articles/PMC5067460/ /pubmed/27751263 http://dx.doi.org/10.1016/j.ihj.2015.09.012 Text en © 2015 Cardiological Society of India. Published by Elsevier B.V. http://creativecommons.org/licenses/by-nc-nd/4.0/ This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/). |
spellingShingle | Case Reports Mohan, Jagdish C. Shukla, Madhu Mohan, Vishwas Sethi, Arvind Parachute mitral valve and Pacman deformity of the ventricular septum in a middle-aged male |
title | Parachute mitral valve and Pacman deformity of the ventricular septum in a middle-aged male |
title_full | Parachute mitral valve and Pacman deformity of the ventricular septum in a middle-aged male |
title_fullStr | Parachute mitral valve and Pacman deformity of the ventricular septum in a middle-aged male |
title_full_unstemmed | Parachute mitral valve and Pacman deformity of the ventricular septum in a middle-aged male |
title_short | Parachute mitral valve and Pacman deformity of the ventricular septum in a middle-aged male |
title_sort | parachute mitral valve and pacman deformity of the ventricular septum in a middle-aged male |
topic | Case Reports |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5067460/ https://www.ncbi.nlm.nih.gov/pubmed/27751263 http://dx.doi.org/10.1016/j.ihj.2015.09.012 |
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