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Parachute mitral valve and Pacman deformity of the ventricular septum in a middle-aged male

Parachute mitral valve and Pacman heart (incomplete muscular ventricular septal defect) are rare congenital deformities usually reported in infants and children. Very few adult patients with these anomalies are reported but the association of the two has not been described. This report describes a 5...

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Autores principales: Mohan, Jagdish C., Shukla, Madhu, Mohan, Vishwas, Sethi, Arvind
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2016
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5067460/
https://www.ncbi.nlm.nih.gov/pubmed/27751263
http://dx.doi.org/10.1016/j.ihj.2015.09.012
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author Mohan, Jagdish C.
Shukla, Madhu
Mohan, Vishwas
Sethi, Arvind
author_facet Mohan, Jagdish C.
Shukla, Madhu
Mohan, Vishwas
Sethi, Arvind
author_sort Mohan, Jagdish C.
collection PubMed
description Parachute mitral valve and Pacman heart (incomplete muscular ventricular septal defect) are rare congenital deformities usually reported in infants and children. Very few adult patients with these anomalies are reported but the association of the two has not been described. This report describes a 56-year-old male with exertional dyspnea who was detected to have moderately severe mitral regurgitation and mitral stenosis. Typical parachute deformity of the mitral valve with a reduced opening and common attachment of all the chordae to a single posteromedial papillary muscle was evident. The chordae were elongated, lax, and redundant, which is atypical for this anomaly. Incidentally, detected aneurysm of the basal muscular interventricular septum (Pacman deformity or incomplete triangular septal defect) was also present.
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spelling pubmed-50674602017-09-01 Parachute mitral valve and Pacman deformity of the ventricular septum in a middle-aged male Mohan, Jagdish C. Shukla, Madhu Mohan, Vishwas Sethi, Arvind Indian Heart J Case Reports Parachute mitral valve and Pacman heart (incomplete muscular ventricular septal defect) are rare congenital deformities usually reported in infants and children. Very few adult patients with these anomalies are reported but the association of the two has not been described. This report describes a 56-year-old male with exertional dyspnea who was detected to have moderately severe mitral regurgitation and mitral stenosis. Typical parachute deformity of the mitral valve with a reduced opening and common attachment of all the chordae to a single posteromedial papillary muscle was evident. The chordae were elongated, lax, and redundant, which is atypical for this anomaly. Incidentally, detected aneurysm of the basal muscular interventricular septum (Pacman deformity or incomplete triangular septal defect) was also present. Elsevier 2016-09 2015-12-22 /pmc/articles/PMC5067460/ /pubmed/27751263 http://dx.doi.org/10.1016/j.ihj.2015.09.012 Text en © 2015 Cardiological Society of India. Published by Elsevier B.V. http://creativecommons.org/licenses/by-nc-nd/4.0/ This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/).
spellingShingle Case Reports
Mohan, Jagdish C.
Shukla, Madhu
Mohan, Vishwas
Sethi, Arvind
Parachute mitral valve and Pacman deformity of the ventricular septum in a middle-aged male
title Parachute mitral valve and Pacman deformity of the ventricular septum in a middle-aged male
title_full Parachute mitral valve and Pacman deformity of the ventricular septum in a middle-aged male
title_fullStr Parachute mitral valve and Pacman deformity of the ventricular septum in a middle-aged male
title_full_unstemmed Parachute mitral valve and Pacman deformity of the ventricular septum in a middle-aged male
title_short Parachute mitral valve and Pacman deformity of the ventricular septum in a middle-aged male
title_sort parachute mitral valve and pacman deformity of the ventricular septum in a middle-aged male
topic Case Reports
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5067460/
https://www.ncbi.nlm.nih.gov/pubmed/27751263
http://dx.doi.org/10.1016/j.ihj.2015.09.012
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