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Multiple osteochondromas (MO) in the forearm: a 12-year single-centre experience

Multiple osteochondromas (MO) are a rare autosomal dominant disorder characterized by the presence of osteochondromas located on the long bones and axial skeleton. Patients present with growth disturbances and angular deformities of the long bones as well as limited motion of affected joints. Forear...

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Autores principales: Ham, John, Flipsen, Mark, Koolen, Marianne, van der Zwan, Arnard, Mader, Konrad
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Springer Milan 2016
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5069205/
https://www.ncbi.nlm.nih.gov/pubmed/27738974
http://dx.doi.org/10.1007/s11751-016-0267-1
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author Ham, John
Flipsen, Mark
Koolen, Marianne
van der Zwan, Arnard
Mader, Konrad
author_facet Ham, John
Flipsen, Mark
Koolen, Marianne
van der Zwan, Arnard
Mader, Konrad
author_sort Ham, John
collection PubMed
description Multiple osteochondromas (MO) are a rare autosomal dominant disorder characterized by the presence of osteochondromas located on the long bones and axial skeleton. Patients present with growth disturbances and angular deformities of the long bones as well as limited motion of affected joints. Forearm involvement is found in a considerable number of patients and may vary from the presence of a simple osteochondroma to severe forearm deformities and radial head dislocation. Patients encounter a variety of problems and symptoms e.g., pain, functional impairment, loss of strength and cosmetic concerns. Several surgical procedures are offered from excision of symptomatic osteochondromas to challenging reconstructions of forearm deformities. We describe visualizing, planning and treating these forearm deformities in MO and, in particular, a detailed account of the surgical correction of Masada type I and Masada type II MO forearm deformities.
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spelling pubmed-50692052016-11-01 Multiple osteochondromas (MO) in the forearm: a 12-year single-centre experience Ham, John Flipsen, Mark Koolen, Marianne van der Zwan, Arnard Mader, Konrad Strategies Trauma Limb Reconstr Original Article Multiple osteochondromas (MO) are a rare autosomal dominant disorder characterized by the presence of osteochondromas located on the long bones and axial skeleton. Patients present with growth disturbances and angular deformities of the long bones as well as limited motion of affected joints. Forearm involvement is found in a considerable number of patients and may vary from the presence of a simple osteochondroma to severe forearm deformities and radial head dislocation. Patients encounter a variety of problems and symptoms e.g., pain, functional impairment, loss of strength and cosmetic concerns. Several surgical procedures are offered from excision of symptomatic osteochondromas to challenging reconstructions of forearm deformities. We describe visualizing, planning and treating these forearm deformities in MO and, in particular, a detailed account of the surgical correction of Masada type I and Masada type II MO forearm deformities. Springer Milan 2016-10-13 2016-11 /pmc/articles/PMC5069205/ /pubmed/27738974 http://dx.doi.org/10.1007/s11751-016-0267-1 Text en © The Author(s) 2016 Open AccessThis article is distributed under the terms of the Creative Commons Attribution 4.0 International License (http://creativecommons.org/licenses/by/4.0/), which permits unrestricted use, distribution, and reproduction in any medium, provided you give appropriate credit to the original author(s) and the source, provide a link to the Creative Commons license, and indicate if changes were made.
spellingShingle Original Article
Ham, John
Flipsen, Mark
Koolen, Marianne
van der Zwan, Arnard
Mader, Konrad
Multiple osteochondromas (MO) in the forearm: a 12-year single-centre experience
title Multiple osteochondromas (MO) in the forearm: a 12-year single-centre experience
title_full Multiple osteochondromas (MO) in the forearm: a 12-year single-centre experience
title_fullStr Multiple osteochondromas (MO) in the forearm: a 12-year single-centre experience
title_full_unstemmed Multiple osteochondromas (MO) in the forearm: a 12-year single-centre experience
title_short Multiple osteochondromas (MO) in the forearm: a 12-year single-centre experience
title_sort multiple osteochondromas (mo) in the forearm: a 12-year single-centre experience
topic Original Article
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5069205/
https://www.ncbi.nlm.nih.gov/pubmed/27738974
http://dx.doi.org/10.1007/s11751-016-0267-1
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