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Modified Atkins diet induces subacute selective ragged‐red‐fiber lysis in mitochondrial myopathy patients

Mitochondrial myopathy (MM) with progressive external ophthalmoplegia (PEO) is a common manifestation of mitochondrial disease in adulthood, for which there is no curative therapy. In mice with MM, ketogenic diet significantly delayed progression of the disease. We asked in this pilot study what eff...

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Detalles Bibliográficos
Autores principales: Ahola, Sofia, Auranen, Mari, Isohanni, Pirjo, Niemisalo, Satu, Urho, Niina, Buzkova, Jana, Velagapudi, Vidya, Lundbom, Nina, Hakkarainen, Antti, Muurinen, Tiina, Piirilä, Päivi, Pietiläinen, Kirsi H, Suomalainen, Anu
Formato: Online Artículo Texto
Lenguaje:English
Publicado: John Wiley and Sons Inc. 2016
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5090657/
https://www.ncbi.nlm.nih.gov/pubmed/27647878
http://dx.doi.org/10.15252/emmm.201606592