Rosai-Dorfman Disease Involving Multiple Organs: An Unusual Case with Poor Prognosis

Rosai-Dorfman disease is a rare, benign histiocytic proliferative disorder that usually affects the lymph nodes. Although extranodal involvement has been reported in diverse sites, manifestation in the cardiovascular system is extremely rare. Specifically, cardiac involvement in Rosai-Dorfman diseas...

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Detalles Bibliográficos
Autores principales: Sendrasoa, Fandresena Arilala, Ranaivo, Irina Mamisoa, Raharolahy, Onivola, Andrianarison, Malalaniaina, Razanakoto, Naina Harinjara, Ramarozatovo, Lala Soavina, Rapelanoro Rabenja, Fahafahantsoa
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Hindawi Publishing Corporation 2016
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5107849/
https://www.ncbi.nlm.nih.gov/pubmed/27872644
http://dx.doi.org/10.1155/2016/3920516
Descripción
Sumario:Rosai-Dorfman disease is a rare, benign histiocytic proliferative disorder that usually affects the lymph nodes. Although extranodal involvement has been reported in diverse sites, manifestation in the cardiovascular system is extremely rare. Specifically, cardiac involvement in Rosai-Dorfman disease is an extraordinarily infrequent event. We describe a case of a 36-year-old female who presented Rosai-Dorfman disease of multiple organs including the heart, with poor prognosis.

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