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Complete agenesis of the dorsal pancreas: A rare clinical entity
Complete agenesis of the dorsal pancreas (ADP) is an exceedingly rare congenital anomaly, compatible with life. The first case was reported in 1911 and so far around 100 cases have been reported in the world literature. Majority of the patients with this anomaly are asymptomatic or associated with a...
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Formato: | Online Artículo Texto |
Lenguaje: | English |
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Medknow Publications & Media Pvt Ltd
2016
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Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5108110/ https://www.ncbi.nlm.nih.gov/pubmed/27857901 http://dx.doi.org/10.4103/2229-516X.192599 |
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author | Robert, Ambooken P Iqbal, Showkathali John, Mathew |
author_facet | Robert, Ambooken P Iqbal, Showkathali John, Mathew |
author_sort | Robert, Ambooken P |
collection | PubMed |
description | Complete agenesis of the dorsal pancreas (ADP) is an exceedingly rare congenital anomaly, compatible with life. The first case was reported in 1911 and so far around 100 cases have been reported in the world literature. Majority of the patients with this anomaly are asymptomatic or associated with abdominal pain, hyperglycemia, diabetes mellitus, and acute or chronic pancreatitis. We present a case report of a 34-year-old male with ADP, diagnosed incidentally during radiological evaluation for abdominal pain. Magnetic resonance cholangiopancreatography confirmed the absence of neck, body, and tail of the pancreas along with duct of Santorini and the minor duodenal papilla. Because of its rarity of occurrence, clinical awareness of the ADP can expand the differential diagnosis and improve patient management in pertinent light of the world literature. |
format | Online Article Text |
id | pubmed-5108110 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2016 |
publisher | Medknow Publications & Media Pvt Ltd |
record_format | MEDLINE/PubMed |
spelling | pubmed-51081102016-11-17 Complete agenesis of the dorsal pancreas: A rare clinical entity Robert, Ambooken P Iqbal, Showkathali John, Mathew Int J Appl Basic Med Res Case Report Complete agenesis of the dorsal pancreas (ADP) is an exceedingly rare congenital anomaly, compatible with life. The first case was reported in 1911 and so far around 100 cases have been reported in the world literature. Majority of the patients with this anomaly are asymptomatic or associated with abdominal pain, hyperglycemia, diabetes mellitus, and acute or chronic pancreatitis. We present a case report of a 34-year-old male with ADP, diagnosed incidentally during radiological evaluation for abdominal pain. Magnetic resonance cholangiopancreatography confirmed the absence of neck, body, and tail of the pancreas along with duct of Santorini and the minor duodenal papilla. Because of its rarity of occurrence, clinical awareness of the ADP can expand the differential diagnosis and improve patient management in pertinent light of the world literature. Medknow Publications & Media Pvt Ltd 2016 /pmc/articles/PMC5108110/ /pubmed/27857901 http://dx.doi.org/10.4103/2229-516X.192599 Text en Copyright: © 2016 International Journal of Applied and Basic Medical Research http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open access article distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 3.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as the author is credited and the new creations are licensed under the identical terms. |
spellingShingle | Case Report Robert, Ambooken P Iqbal, Showkathali John, Mathew Complete agenesis of the dorsal pancreas: A rare clinical entity |
title | Complete agenesis of the dorsal pancreas: A rare clinical entity |
title_full | Complete agenesis of the dorsal pancreas: A rare clinical entity |
title_fullStr | Complete agenesis of the dorsal pancreas: A rare clinical entity |
title_full_unstemmed | Complete agenesis of the dorsal pancreas: A rare clinical entity |
title_short | Complete agenesis of the dorsal pancreas: A rare clinical entity |
title_sort | complete agenesis of the dorsal pancreas: a rare clinical entity |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5108110/ https://www.ncbi.nlm.nih.gov/pubmed/27857901 http://dx.doi.org/10.4103/2229-516X.192599 |
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