Right Lung Agenesis with Tracheal Stenosis due to Complete Tracheal Rings and Postpneumonectomy Like Syndrome Treated with Tissue Expander Placement

Congenital lung agenesis is an extremely rare condition with an estimated prevalence of 34 in 1,000,000 live births. It is often associated with other congenital malformations of the skeletal, cardiovascular, urogenital, and gastrointestinal systems. We discuss the case of a 5-month-old who presente...

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Autores principales: Agrawal, Yashwant, Patri, Sandeep, Kalavakunta, Jagadeesh K.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Hindawi Publishing Corporation 2016
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5108851/
https://www.ncbi.nlm.nih.gov/pubmed/27882259
http://dx.doi.org/10.1155/2016/4397641
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author Agrawal, Yashwant
Patri, Sandeep
Kalavakunta, Jagadeesh K.
author_facet Agrawal, Yashwant
Patri, Sandeep
Kalavakunta, Jagadeesh K.
author_sort Agrawal, Yashwant
collection PubMed
description Congenital lung agenesis is an extremely rare condition with an estimated prevalence of 34 in 1,000,000 live births. It is often associated with other congenital malformations of the skeletal, cardiovascular, urogenital, and gastrointestinal systems. We discuss the case of a 5-month-old who presented with increasing stridor over 1 month. Imaging revealed right lung agenesis, complete dextromalposition of heart, and compression of distal trachea. An intrathoracic saline tissue expander was placed which marked improved distal tracheal stenosis. In patients who are symptomatic it becomes imperative to perform surgeries to increase survival as was the case in this patient.
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spelling pubmed-51088512016-11-23 Right Lung Agenesis with Tracheal Stenosis due to Complete Tracheal Rings and Postpneumonectomy Like Syndrome Treated with Tissue Expander Placement Agrawal, Yashwant Patri, Sandeep Kalavakunta, Jagadeesh K. Case Rep Pulmonol Case Report Congenital lung agenesis is an extremely rare condition with an estimated prevalence of 34 in 1,000,000 live births. It is often associated with other congenital malformations of the skeletal, cardiovascular, urogenital, and gastrointestinal systems. We discuss the case of a 5-month-old who presented with increasing stridor over 1 month. Imaging revealed right lung agenesis, complete dextromalposition of heart, and compression of distal trachea. An intrathoracic saline tissue expander was placed which marked improved distal tracheal stenosis. In patients who are symptomatic it becomes imperative to perform surgeries to increase survival as was the case in this patient. Hindawi Publishing Corporation 2016 2016-11-01 /pmc/articles/PMC5108851/ /pubmed/27882259 http://dx.doi.org/10.1155/2016/4397641 Text en Copyright © 2016 Yashwant Agrawal et al. https://creativecommons.org/licenses/by/4.0/ This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Agrawal, Yashwant
Patri, Sandeep
Kalavakunta, Jagadeesh K.
Right Lung Agenesis with Tracheal Stenosis due to Complete Tracheal Rings and Postpneumonectomy Like Syndrome Treated with Tissue Expander Placement
title Right Lung Agenesis with Tracheal Stenosis due to Complete Tracheal Rings and Postpneumonectomy Like Syndrome Treated with Tissue Expander Placement
title_full Right Lung Agenesis with Tracheal Stenosis due to Complete Tracheal Rings and Postpneumonectomy Like Syndrome Treated with Tissue Expander Placement
title_fullStr Right Lung Agenesis with Tracheal Stenosis due to Complete Tracheal Rings and Postpneumonectomy Like Syndrome Treated with Tissue Expander Placement
title_full_unstemmed Right Lung Agenesis with Tracheal Stenosis due to Complete Tracheal Rings and Postpneumonectomy Like Syndrome Treated with Tissue Expander Placement
title_short Right Lung Agenesis with Tracheal Stenosis due to Complete Tracheal Rings and Postpneumonectomy Like Syndrome Treated with Tissue Expander Placement
title_sort right lung agenesis with tracheal stenosis due to complete tracheal rings and postpneumonectomy like syndrome treated with tissue expander placement
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5108851/
https://www.ncbi.nlm.nih.gov/pubmed/27882259
http://dx.doi.org/10.1155/2016/4397641
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