Cargando…

Recurrent Cholangitis in a Patient with Autosomal Dominant Polycystic Kidney Disease (ADPKD) and Caroli's Disease

We herein present a rare case of an autosomal dominant polycystic kidney disease (ADPKD) patient with Caroli's disease, a congenital embryonic biliary tree ductal plate abnormality often associated with autosomal recessive polycystic kidney disease. A 76-year-old woman with ADPKD on hemodialysi...

Descripción completa

Detalles Bibliográficos
Autores principales: Hasegawa, Eiko, Sawa, Naoki, Hoshino, Junichi, Suwabe, Tatsuya, Hayami, Noriko, Yamanouchi, Masayuki, Sekine, Akinari, Hiramatsu, Rikako, Imafuku, Aya, Kawada, Masahiro, Ubara, Yoshifumi, Imamura, Tsunao, Takaichi, Kenmei
Formato: Online Artículo Texto
Lenguaje:English
Publicado: The Japanese Society of Internal Medicine 2016
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5109570/
https://www.ncbi.nlm.nih.gov/pubmed/27746440
_version_ 1782467568038051840
author Hasegawa, Eiko
Sawa, Naoki
Hoshino, Junichi
Suwabe, Tatsuya
Hayami, Noriko
Yamanouchi, Masayuki
Sekine, Akinari
Hiramatsu, Rikako
Imafuku, Aya
Kawada, Masahiro
Ubara, Yoshifumi
Imamura, Tsunao
Takaichi, Kenmei
author_facet Hasegawa, Eiko
Sawa, Naoki
Hoshino, Junichi
Suwabe, Tatsuya
Hayami, Noriko
Yamanouchi, Masayuki
Sekine, Akinari
Hiramatsu, Rikako
Imafuku, Aya
Kawada, Masahiro
Ubara, Yoshifumi
Imamura, Tsunao
Takaichi, Kenmei
author_sort Hasegawa, Eiko
collection PubMed
description We herein present a rare case of an autosomal dominant polycystic kidney disease (ADPKD) patient with Caroli's disease, a congenital embryonic biliary tree ductal plate abnormality often associated with autosomal recessive polycystic kidney disease. A 76-year-old woman with ADPKD on hemodialysis was admitted to our hospital with recurrent cholangitis and hepatobiliary stones. Caroli's disease was diagnosed according to typical imaging findings of cystic intrahepatic bile duct dilatation and the central dot sign. Hepatobiliary system abnormalities such as Caroli's disease should be considered in febrile ADPKD patients, even in the absence of typical clinical signs or symptoms.
format Online
Article
Text
id pubmed-5109570
institution National Center for Biotechnology Information
language English
publishDate 2016
publisher The Japanese Society of Internal Medicine
record_format MEDLINE/PubMed
spelling pubmed-51095702016-11-17 Recurrent Cholangitis in a Patient with Autosomal Dominant Polycystic Kidney Disease (ADPKD) and Caroli's Disease Hasegawa, Eiko Sawa, Naoki Hoshino, Junichi Suwabe, Tatsuya Hayami, Noriko Yamanouchi, Masayuki Sekine, Akinari Hiramatsu, Rikako Imafuku, Aya Kawada, Masahiro Ubara, Yoshifumi Imamura, Tsunao Takaichi, Kenmei Intern Med Case Report We herein present a rare case of an autosomal dominant polycystic kidney disease (ADPKD) patient with Caroli's disease, a congenital embryonic biliary tree ductal plate abnormality often associated with autosomal recessive polycystic kidney disease. A 76-year-old woman with ADPKD on hemodialysis was admitted to our hospital with recurrent cholangitis and hepatobiliary stones. Caroli's disease was diagnosed according to typical imaging findings of cystic intrahepatic bile duct dilatation and the central dot sign. Hepatobiliary system abnormalities such as Caroli's disease should be considered in febrile ADPKD patients, even in the absence of typical clinical signs or symptoms. The Japanese Society of Internal Medicine 2016-10-15 /pmc/articles/PMC5109570/ /pubmed/27746440 Text en https://creativecommons.org/licenses/by-nc-nd/4.0/ The Internal Medicine is an Open Access article distributed under the Creative Commons Attribution-NonCommercial-NoDerivatives 4.0 International License. To view the details of this license, please visit (https://creativecommons.org/licenses/by-nc-nd/4.0/).
spellingShingle Case Report
Hasegawa, Eiko
Sawa, Naoki
Hoshino, Junichi
Suwabe, Tatsuya
Hayami, Noriko
Yamanouchi, Masayuki
Sekine, Akinari
Hiramatsu, Rikako
Imafuku, Aya
Kawada, Masahiro
Ubara, Yoshifumi
Imamura, Tsunao
Takaichi, Kenmei
Recurrent Cholangitis in a Patient with Autosomal Dominant Polycystic Kidney Disease (ADPKD) and Caroli's Disease
title Recurrent Cholangitis in a Patient with Autosomal Dominant Polycystic Kidney Disease (ADPKD) and Caroli's Disease
title_full Recurrent Cholangitis in a Patient with Autosomal Dominant Polycystic Kidney Disease (ADPKD) and Caroli's Disease
title_fullStr Recurrent Cholangitis in a Patient with Autosomal Dominant Polycystic Kidney Disease (ADPKD) and Caroli's Disease
title_full_unstemmed Recurrent Cholangitis in a Patient with Autosomal Dominant Polycystic Kidney Disease (ADPKD) and Caroli's Disease
title_short Recurrent Cholangitis in a Patient with Autosomal Dominant Polycystic Kidney Disease (ADPKD) and Caroli's Disease
title_sort recurrent cholangitis in a patient with autosomal dominant polycystic kidney disease (adpkd) and caroli's disease
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5109570/
https://www.ncbi.nlm.nih.gov/pubmed/27746440
work_keys_str_mv AT hasegawaeiko recurrentcholangitisinapatientwithautosomaldominantpolycystickidneydiseaseadpkdandcarolisdisease
AT sawanaoki recurrentcholangitisinapatientwithautosomaldominantpolycystickidneydiseaseadpkdandcarolisdisease
AT hoshinojunichi recurrentcholangitisinapatientwithautosomaldominantpolycystickidneydiseaseadpkdandcarolisdisease
AT suwabetatsuya recurrentcholangitisinapatientwithautosomaldominantpolycystickidneydiseaseadpkdandcarolisdisease
AT hayaminoriko recurrentcholangitisinapatientwithautosomaldominantpolycystickidneydiseaseadpkdandcarolisdisease
AT yamanouchimasayuki recurrentcholangitisinapatientwithautosomaldominantpolycystickidneydiseaseadpkdandcarolisdisease
AT sekineakinari recurrentcholangitisinapatientwithautosomaldominantpolycystickidneydiseaseadpkdandcarolisdisease
AT hiramatsurikako recurrentcholangitisinapatientwithautosomaldominantpolycystickidneydiseaseadpkdandcarolisdisease
AT imafukuaya recurrentcholangitisinapatientwithautosomaldominantpolycystickidneydiseaseadpkdandcarolisdisease
AT kawadamasahiro recurrentcholangitisinapatientwithautosomaldominantpolycystickidneydiseaseadpkdandcarolisdisease
AT ubarayoshifumi recurrentcholangitisinapatientwithautosomaldominantpolycystickidneydiseaseadpkdandcarolisdisease
AT imamuratsunao recurrentcholangitisinapatientwithautosomaldominantpolycystickidneydiseaseadpkdandcarolisdisease
AT takaichikenmei recurrentcholangitisinapatientwithautosomaldominantpolycystickidneydiseaseadpkdandcarolisdisease