Cargando…
Recurrent Cholangitis in a Patient with Autosomal Dominant Polycystic Kidney Disease (ADPKD) and Caroli's Disease
We herein present a rare case of an autosomal dominant polycystic kidney disease (ADPKD) patient with Caroli's disease, a congenital embryonic biliary tree ductal plate abnormality often associated with autosomal recessive polycystic kidney disease. A 76-year-old woman with ADPKD on hemodialysi...
Autores principales: | , , , , , , , , , , , , |
---|---|
Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
The Japanese Society of Internal Medicine
2016
|
Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5109570/ https://www.ncbi.nlm.nih.gov/pubmed/27746440 |
_version_ | 1782467568038051840 |
---|---|
author | Hasegawa, Eiko Sawa, Naoki Hoshino, Junichi Suwabe, Tatsuya Hayami, Noriko Yamanouchi, Masayuki Sekine, Akinari Hiramatsu, Rikako Imafuku, Aya Kawada, Masahiro Ubara, Yoshifumi Imamura, Tsunao Takaichi, Kenmei |
author_facet | Hasegawa, Eiko Sawa, Naoki Hoshino, Junichi Suwabe, Tatsuya Hayami, Noriko Yamanouchi, Masayuki Sekine, Akinari Hiramatsu, Rikako Imafuku, Aya Kawada, Masahiro Ubara, Yoshifumi Imamura, Tsunao Takaichi, Kenmei |
author_sort | Hasegawa, Eiko |
collection | PubMed |
description | We herein present a rare case of an autosomal dominant polycystic kidney disease (ADPKD) patient with Caroli's disease, a congenital embryonic biliary tree ductal plate abnormality often associated with autosomal recessive polycystic kidney disease. A 76-year-old woman with ADPKD on hemodialysis was admitted to our hospital with recurrent cholangitis and hepatobiliary stones. Caroli's disease was diagnosed according to typical imaging findings of cystic intrahepatic bile duct dilatation and the central dot sign. Hepatobiliary system abnormalities such as Caroli's disease should be considered in febrile ADPKD patients, even in the absence of typical clinical signs or symptoms. |
format | Online Article Text |
id | pubmed-5109570 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2016 |
publisher | The Japanese Society of Internal Medicine |
record_format | MEDLINE/PubMed |
spelling | pubmed-51095702016-11-17 Recurrent Cholangitis in a Patient with Autosomal Dominant Polycystic Kidney Disease (ADPKD) and Caroli's Disease Hasegawa, Eiko Sawa, Naoki Hoshino, Junichi Suwabe, Tatsuya Hayami, Noriko Yamanouchi, Masayuki Sekine, Akinari Hiramatsu, Rikako Imafuku, Aya Kawada, Masahiro Ubara, Yoshifumi Imamura, Tsunao Takaichi, Kenmei Intern Med Case Report We herein present a rare case of an autosomal dominant polycystic kidney disease (ADPKD) patient with Caroli's disease, a congenital embryonic biliary tree ductal plate abnormality often associated with autosomal recessive polycystic kidney disease. A 76-year-old woman with ADPKD on hemodialysis was admitted to our hospital with recurrent cholangitis and hepatobiliary stones. Caroli's disease was diagnosed according to typical imaging findings of cystic intrahepatic bile duct dilatation and the central dot sign. Hepatobiliary system abnormalities such as Caroli's disease should be considered in febrile ADPKD patients, even in the absence of typical clinical signs or symptoms. The Japanese Society of Internal Medicine 2016-10-15 /pmc/articles/PMC5109570/ /pubmed/27746440 Text en https://creativecommons.org/licenses/by-nc-nd/4.0/ The Internal Medicine is an Open Access article distributed under the Creative Commons Attribution-NonCommercial-NoDerivatives 4.0 International License. To view the details of this license, please visit (https://creativecommons.org/licenses/by-nc-nd/4.0/). |
spellingShingle | Case Report Hasegawa, Eiko Sawa, Naoki Hoshino, Junichi Suwabe, Tatsuya Hayami, Noriko Yamanouchi, Masayuki Sekine, Akinari Hiramatsu, Rikako Imafuku, Aya Kawada, Masahiro Ubara, Yoshifumi Imamura, Tsunao Takaichi, Kenmei Recurrent Cholangitis in a Patient with Autosomal Dominant Polycystic Kidney Disease (ADPKD) and Caroli's Disease |
title | Recurrent Cholangitis in a Patient with Autosomal Dominant Polycystic Kidney Disease (ADPKD) and Caroli's Disease |
title_full | Recurrent Cholangitis in a Patient with Autosomal Dominant Polycystic Kidney Disease (ADPKD) and Caroli's Disease |
title_fullStr | Recurrent Cholangitis in a Patient with Autosomal Dominant Polycystic Kidney Disease (ADPKD) and Caroli's Disease |
title_full_unstemmed | Recurrent Cholangitis in a Patient with Autosomal Dominant Polycystic Kidney Disease (ADPKD) and Caroli's Disease |
title_short | Recurrent Cholangitis in a Patient with Autosomal Dominant Polycystic Kidney Disease (ADPKD) and Caroli's Disease |
title_sort | recurrent cholangitis in a patient with autosomal dominant polycystic kidney disease (adpkd) and caroli's disease |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5109570/ https://www.ncbi.nlm.nih.gov/pubmed/27746440 |
work_keys_str_mv | AT hasegawaeiko recurrentcholangitisinapatientwithautosomaldominantpolycystickidneydiseaseadpkdandcarolisdisease AT sawanaoki recurrentcholangitisinapatientwithautosomaldominantpolycystickidneydiseaseadpkdandcarolisdisease AT hoshinojunichi recurrentcholangitisinapatientwithautosomaldominantpolycystickidneydiseaseadpkdandcarolisdisease AT suwabetatsuya recurrentcholangitisinapatientwithautosomaldominantpolycystickidneydiseaseadpkdandcarolisdisease AT hayaminoriko recurrentcholangitisinapatientwithautosomaldominantpolycystickidneydiseaseadpkdandcarolisdisease AT yamanouchimasayuki recurrentcholangitisinapatientwithautosomaldominantpolycystickidneydiseaseadpkdandcarolisdisease AT sekineakinari recurrentcholangitisinapatientwithautosomaldominantpolycystickidneydiseaseadpkdandcarolisdisease AT hiramatsurikako recurrentcholangitisinapatientwithautosomaldominantpolycystickidneydiseaseadpkdandcarolisdisease AT imafukuaya recurrentcholangitisinapatientwithautosomaldominantpolycystickidneydiseaseadpkdandcarolisdisease AT kawadamasahiro recurrentcholangitisinapatientwithautosomaldominantpolycystickidneydiseaseadpkdandcarolisdisease AT ubarayoshifumi recurrentcholangitisinapatientwithautosomaldominantpolycystickidneydiseaseadpkdandcarolisdisease AT imamuratsunao recurrentcholangitisinapatientwithautosomaldominantpolycystickidneydiseaseadpkdandcarolisdisease AT takaichikenmei recurrentcholangitisinapatientwithautosomaldominantpolycystickidneydiseaseadpkdandcarolisdisease |