Steroid Responsive Mononeuritis Multiplex in the Cronkhite–Canada Syndrome

The Cronkhite–Canada syndrome (CCS) is a rare disorder of unknown origin characterized by generalized gastrointestinal polyposis, alopecia, hyperpigmentation, and onychodystrophy. We report a case of CCS with concomitant presentation of mononeuritis multiplex. The electrophysiological findings and s...

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Detalles Bibliográficos
Autores principales: Lo, Y. L., Lim, K. H., Cheng, X. M., Mesenas, S.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Frontiers Media S.A. 2016
Materias:
Neuroscience
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5110953/
https://www.ncbi.nlm.nih.gov/pubmed/27899913
http://dx.doi.org/10.3389/fneur.2016.00207
Descripción
Sumario:The Cronkhite–Canada syndrome (CCS) is a rare disorder of unknown origin characterized by generalized gastrointestinal polyposis, alopecia, hyperpigmentation, and onychodystrophy. We report a case of CCS with concomitant presentation of mononeuritis multiplex. The electrophysiological findings and steroid responsiveness suggests presence of an autoimmune mechanism.

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