Steroid Responsive Mononeuritis Multiplex in the Cronkhite–Canada Syndrome

The Cronkhite–Canada syndrome (CCS) is a rare disorder of unknown origin characterized by generalized gastrointestinal polyposis, alopecia, hyperpigmentation, and onychodystrophy. We report a case of CCS with concomitant presentation of mononeuritis multiplex. The electrophysiological findings and s...

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Detalles Bibliográficos
Autores principales: Lo, Y. L., Lim, K. H., Cheng, X. M., Mesenas, S.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Frontiers Media S.A. 2016
Materias:
Neuroscience
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5110953/
https://www.ncbi.nlm.nih.gov/pubmed/27899913
http://dx.doi.org/10.3389/fneur.2016.00207
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author Lo, Y. L.
Lim, K. H.
Cheng, X. M.
Mesenas, S.
author_facet Lo, Y. L.
Lim, K. H.
Cheng, X. M.
Mesenas, S.
author_sort Lo, Y. L.
collection PubMed
description The Cronkhite–Canada syndrome (CCS) is a rare disorder of unknown origin characterized by generalized gastrointestinal polyposis, alopecia, hyperpigmentation, and onychodystrophy. We report a case of CCS with concomitant presentation of mononeuritis multiplex. The electrophysiological findings and steroid responsiveness suggests presence of an autoimmune mechanism.
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spelling pubmed-51109532016-11-29 Steroid Responsive Mononeuritis Multiplex in the Cronkhite–Canada Syndrome Lo, Y. L. Lim, K. H. Cheng, X. M. Mesenas, S. Front Neurol Neuroscience The Cronkhite–Canada syndrome (CCS) is a rare disorder of unknown origin characterized by generalized gastrointestinal polyposis, alopecia, hyperpigmentation, and onychodystrophy. We report a case of CCS with concomitant presentation of mononeuritis multiplex. The electrophysiological findings and steroid responsiveness suggests presence of an autoimmune mechanism. Frontiers Media S.A. 2016-11-17 /pmc/articles/PMC5110953/ /pubmed/27899913 http://dx.doi.org/10.3389/fneur.2016.00207 Text en Copyright © 2016 Lo, Lim, Cheng and Mesenas. http://creativecommons.org/licenses/by/4.0/ This is an open-access article distributed under the terms of the Creative Commons Attribution License (CC BY). The use, distribution or reproduction in other forums is permitted, provided the original author(s) or licensor are credited and that the original publication in this journal is cited, in accordance with accepted academic practice. No use, distribution or reproduction is permitted which does not comply with these terms.
spellingShingle Neuroscience
Lo, Y. L.
Lim, K. H.
Cheng, X. M.
Mesenas, S.
Steroid Responsive Mononeuritis Multiplex in the Cronkhite–Canada Syndrome
title Steroid Responsive Mononeuritis Multiplex in the Cronkhite–Canada Syndrome
title_full Steroid Responsive Mononeuritis Multiplex in the Cronkhite–Canada Syndrome
title_fullStr Steroid Responsive Mononeuritis Multiplex in the Cronkhite–Canada Syndrome
title_full_unstemmed Steroid Responsive Mononeuritis Multiplex in the Cronkhite–Canada Syndrome
title_short Steroid Responsive Mononeuritis Multiplex in the Cronkhite–Canada Syndrome
title_sort steroid responsive mononeuritis multiplex in the cronkhite–canada syndrome
topic Neuroscience
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5110953/
https://www.ncbi.nlm.nih.gov/pubmed/27899913
http://dx.doi.org/10.3389/fneur.2016.00207
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AT mesenass steroidresponsivemononeuritismultiplexinthecronkhitecanadasyndrome

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