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Encephalocraniocutaneous lipomatosis (Haberland syndrome): A rare case report
Haberland syndrome or Fishman syndrome also known as encephalocraniocutaneous lipomatosis (ECCL) is a rare, congenital neurocutaneous disorder. It is characterized by unilateral involvement of skin, eyes and central nervous system. We report the case of a 28-year-old woman who presented with soft li...
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Formato: | Online Artículo Texto |
Lenguaje: | English |
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Medknow Publications & Media Pvt Ltd
2016
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Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5134170/ https://www.ncbi.nlm.nih.gov/pubmed/27990391 http://dx.doi.org/10.4103/2229-5178.193901 |
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author | Jagati, Ashish Shah, Bela J. Joshi, Rima Gajjar, Trusha |
author_facet | Jagati, Ashish Shah, Bela J. Joshi, Rima Gajjar, Trusha |
author_sort | Jagati, Ashish |
collection | PubMed |
description | Haberland syndrome or Fishman syndrome also known as encephalocraniocutaneous lipomatosis (ECCL) is a rare, congenital neurocutaneous disorder. It is characterized by unilateral involvement of skin, eyes and central nervous system. We report the case of a 28-year-old woman who presented with soft lipomatous swelling over right temporal area with nonscarring alopecia of part of frontal and parietal region. The patient had a history of seizures and ipsilateral scleral dermoid. Computed tomography scan findings were suggestive of lipomas and calcification of falx. Magnetic resonance imaging showed right-sided hemi atrophy and two intracranial cysts. We report this case because of its rarity. |
format | Online Article Text |
id | pubmed-5134170 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2016 |
publisher | Medknow Publications & Media Pvt Ltd |
record_format | MEDLINE/PubMed |
spelling | pubmed-51341702016-12-16 Encephalocraniocutaneous lipomatosis (Haberland syndrome): A rare case report Jagati, Ashish Shah, Bela J. Joshi, Rima Gajjar, Trusha Indian Dermatol Online J Case Report Haberland syndrome or Fishman syndrome also known as encephalocraniocutaneous lipomatosis (ECCL) is a rare, congenital neurocutaneous disorder. It is characterized by unilateral involvement of skin, eyes and central nervous system. We report the case of a 28-year-old woman who presented with soft lipomatous swelling over right temporal area with nonscarring alopecia of part of frontal and parietal region. The patient had a history of seizures and ipsilateral scleral dermoid. Computed tomography scan findings were suggestive of lipomas and calcification of falx. Magnetic resonance imaging showed right-sided hemi atrophy and two intracranial cysts. We report this case because of its rarity. Medknow Publications & Media Pvt Ltd 2016 /pmc/articles/PMC5134170/ /pubmed/27990391 http://dx.doi.org/10.4103/2229-5178.193901 Text en Copyright: © Indian Dermatology Online Journal http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open access article distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 3.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as the author is credited and the new creations are licensed under the identical terms. |
spellingShingle | Case Report Jagati, Ashish Shah, Bela J. Joshi, Rima Gajjar, Trusha Encephalocraniocutaneous lipomatosis (Haberland syndrome): A rare case report |
title | Encephalocraniocutaneous lipomatosis (Haberland syndrome): A rare case report |
title_full | Encephalocraniocutaneous lipomatosis (Haberland syndrome): A rare case report |
title_fullStr | Encephalocraniocutaneous lipomatosis (Haberland syndrome): A rare case report |
title_full_unstemmed | Encephalocraniocutaneous lipomatosis (Haberland syndrome): A rare case report |
title_short | Encephalocraniocutaneous lipomatosis (Haberland syndrome): A rare case report |
title_sort | encephalocraniocutaneous lipomatosis (haberland syndrome): a rare case report |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5134170/ https://www.ncbi.nlm.nih.gov/pubmed/27990391 http://dx.doi.org/10.4103/2229-5178.193901 |
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