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The Mitochondrial m-AAA Protease Prevents Demyelination and Hair Greying

The m-AAA protease preserves proteostasis of the inner mitochondrial membrane. It ensures a functional respiratory chain, by controlling the turnover of respiratory complex subunits and allowing mitochondrial translation, but other functions in mitochondria are conceivable. Mutations in genes encodi...

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Detalles Bibliográficos
Autores principales:	Wang, Shuaiyu, Jacquemyn, Julie, Murru, Sara, Martinelli, Paola, Barth, Esther, Langer, Thomas, Niessen, Carien M., Rugarli, Elena I.
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Public Library of Science 2016
Materias:	Research Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5135034/ https://www.ncbi.nlm.nih.gov/pubmed/27911893 http://dx.doi.org/10.1371/journal.pgen.1006463

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