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What do we know about pulmonary blastoma?: review of literature and clinical case report

Pulmonary blastoma (PB) is a rare form of lung tumour and is accountable for 0.25–0.5% of primary pulmonary malignancies. Initially pulmonary blastoma was divided into three subtypes: biphasic pulmonary blastoma (BPB) consisting of an epithelial and mesenchymal component, well differentiated fetal a...

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Detalles Bibliográficos
Autores principales: Brodowska-Kania, Dorota, Kotwica, Ewa, Paturej, Aleksandra, Sośnicki, Witold, Patera, Janusz, Giżewska, Agnieszka, Niemczyk, Stanisław
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Nagoya University 2016
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5159477/
https://www.ncbi.nlm.nih.gov/pubmed/28008207
http://dx.doi.org/10.18999/nagjms.78.4.507
Descripción
Sumario:Pulmonary blastoma (PB) is a rare form of lung tumour and is accountable for 0.25–0.5% of primary pulmonary malignancies. Initially pulmonary blastoma was divided into three subtypes: biphasic pulmonary blastoma (BPB) consisting of an epithelial and mesenchymal component, well differentiated fetal adenocarcinoma (WDFA) built of well differentiated epithelium and a mesenchymal component and malignant pleuropulmonary blastoma (PPB). Prognosis in this type of cancer is really poor. We present a current review of literature and a clinical case report. Treatment of PB is very difficult. Data and recommendations about the treatment of pulmonary blastoma are still available therefore we should use only observations and clinical case reports.