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Advances in the management of erythropoietic protoporphyria – role of afamelanotide

Erythropoietic protoporphyria (EPP) and the phenotypically similar disease X-linked protoporphyria (XLPP) are inherited cutaneous porphyrias characterized clinically by acute non-blistering photosensitivity, intolerance to sunlight, and significantly reduced quality of life. They are due to marked o...

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Detalles Bibliográficos
Autores principales:	Lane, Ashley M, McKay, Jerome T, Bonkovsky, Herbert L
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Dove Medical Press 2016
Materias:	Review
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5161401/ https://www.ncbi.nlm.nih.gov/pubmed/28003770 http://dx.doi.org/10.2147/TACG.S122030

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