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Autophagy activation in COL6 myopathic patients by a low-protein-diet pilot trial

A pilot clinical trial based on nutritional modulation was designed to assess the efficacy of a one-year low-protein diet in activating autophagy in skeletal muscle of patients affected by COL6/collagen VI-related myopathies. Ullrich congenital muscular dystrophy and Bethlem myopathy are rare inheri...

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Detalles Bibliográficos
Autores principales: Castagnaro, Silvia, Pellegrini, Camilla, Pellegrini, Massimo, Chrisam, Martina, Sabatelli, Patrizia, Toni, Silvia, Grumati, Paolo, Ripamonti, Claudio, Pratelli, Loredana, Maraldi, Nadir M., Cocchi, Daniela, Righi, Valeria, Faldini, Cesare, Sandri, Marco, Bonaldo, Paolo, Merlini, Luciano
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Taylor & Francis 2016
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5173266/
https://www.ncbi.nlm.nih.gov/pubmed/27656840
http://dx.doi.org/10.1080/15548627.2016.1231279