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Autophagy activation in COL6 myopathic patients by a low-protein-diet pilot trial
A pilot clinical trial based on nutritional modulation was designed to assess the efficacy of a one-year low-protein diet in activating autophagy in skeletal muscle of patients affected by COL6/collagen VI-related myopathies. Ullrich congenital muscular dystrophy and Bethlem myopathy are rare inheri...
Autores principales: | Castagnaro, Silvia, Pellegrini, Camilla, Pellegrini, Massimo, Chrisam, Martina, Sabatelli, Patrizia, Toni, Silvia, Grumati, Paolo, Ripamonti, Claudio, Pratelli, Loredana, Maraldi, Nadir M., Cocchi, Daniela, Righi, Valeria, Faldini, Cesare, Sandri, Marco, Bonaldo, Paolo, Merlini, Luciano |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Taylor & Francis
2016
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5173266/ https://www.ncbi.nlm.nih.gov/pubmed/27656840 http://dx.doi.org/10.1080/15548627.2016.1231279 |
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