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A rare malignancy in a patient with neurofibromatosis: gastric adenocarcinoma

Neurofibromatosis is an autosomal dominant disease that is characterized by cutaneous hyperpigmentation and multiple neurofibromas and often accompanied by localized peripheral and central neural tumors. Gastrointestinal involvement is seen in 25% of the cases. Gastrointestinal stromal tumors, pancr...

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Detalles Bibliográficos
Autores principales: Barut, Bora, Ince, Volkan, Ozdemir, Fatih, Harputluoglu, Murat, Isik, Burak
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Kare Publishing 2015
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5175097/
https://www.ncbi.nlm.nih.gov/pubmed/28058360
http://dx.doi.org/10.14744/nci.2015.33042
Descripción
Sumario:Neurofibromatosis is an autosomal dominant disease that is characterized by cutaneous hyperpigmentation and multiple neurofibromas and often accompanied by localized peripheral and central neural tumors. Gastrointestinal involvement is seen in 25% of the cases. Gastrointestinal stromal tumors, pancreatic and duodenal neuroendocrine tumors are the most common tumors in patients with neurofibromatosis. Neurofibromatosis and gastric adenocarcinoma constitute an extremely rare combination. In this case report we aim to present a patient with neurofibromatosis operated due to gastric adenocarcinoma.