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Successful outcome of three patients with sickle‐cell disease and fat embolism syndrome treated with intensive exchange transfusion
Fat embolism syndrome (FES) is a rare complication of sickle‐cell disease (SCD) associated with extremely high mortality rates. It affects predominantly non‐SS patients and those with previously mild disease. Rapid institution of exchange transfusion with an aim to reduce HbS to very low levels as s...
Autores principales: | , , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
John Wiley and Sons Inc.
2016
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5224784/ https://www.ncbi.nlm.nih.gov/pubmed/28096988 http://dx.doi.org/10.1002/ccr3.727 |
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author | Greaves, Paul Mathew, Vivek Peters, Catherine Rowe, Susan Amos, Roger J. Tsitsikas, Dimitris A. |
author_facet | Greaves, Paul Mathew, Vivek Peters, Catherine Rowe, Susan Amos, Roger J. Tsitsikas, Dimitris A. |
author_sort | Greaves, Paul |
collection | PubMed |
description | Fat embolism syndrome (FES) is a rare complication of sickle‐cell disease (SCD) associated with extremely high mortality rates. It affects predominantly non‐SS patients and those with previously mild disease. Rapid institution of exchange transfusion with an aim to reduce HbS to very low levels as soon as FES is suspected can be life‐saving. |
format | Online Article Text |
id | pubmed-5224784 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2016 |
publisher | John Wiley and Sons Inc. |
record_format | MEDLINE/PubMed |
spelling | pubmed-52247842017-01-17 Successful outcome of three patients with sickle‐cell disease and fat embolism syndrome treated with intensive exchange transfusion Greaves, Paul Mathew, Vivek Peters, Catherine Rowe, Susan Amos, Roger J. Tsitsikas, Dimitris A. Clin Case Rep Case Reports Fat embolism syndrome (FES) is a rare complication of sickle‐cell disease (SCD) associated with extremely high mortality rates. It affects predominantly non‐SS patients and those with previously mild disease. Rapid institution of exchange transfusion with an aim to reduce HbS to very low levels as soon as FES is suspected can be life‐saving. John Wiley and Sons Inc. 2016-12-20 /pmc/articles/PMC5224784/ /pubmed/28096988 http://dx.doi.org/10.1002/ccr3.727 Text en © 2016 The Authors. Clinical Case Reports published by John Wiley & Sons Ltd. This is an open access article under the terms of the Creative Commons Attribution‐NonCommercial‐NoDerivs (http://creativecommons.org/licenses/by-nc-nd/4.0/) License, which permits use and distribution in any medium, provided the original work is properly cited, the use is non‐commercial and no modifications or adaptations are made. |
spellingShingle | Case Reports Greaves, Paul Mathew, Vivek Peters, Catherine Rowe, Susan Amos, Roger J. Tsitsikas, Dimitris A. Successful outcome of three patients with sickle‐cell disease and fat embolism syndrome treated with intensive exchange transfusion |
title | Successful outcome of three patients with sickle‐cell disease and fat embolism syndrome treated with intensive exchange transfusion |
title_full | Successful outcome of three patients with sickle‐cell disease and fat embolism syndrome treated with intensive exchange transfusion |
title_fullStr | Successful outcome of three patients with sickle‐cell disease and fat embolism syndrome treated with intensive exchange transfusion |
title_full_unstemmed | Successful outcome of three patients with sickle‐cell disease and fat embolism syndrome treated with intensive exchange transfusion |
title_short | Successful outcome of three patients with sickle‐cell disease and fat embolism syndrome treated with intensive exchange transfusion |
title_sort | successful outcome of three patients with sickle‐cell disease and fat embolism syndrome treated with intensive exchange transfusion |
topic | Case Reports |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5224784/ https://www.ncbi.nlm.nih.gov/pubmed/28096988 http://dx.doi.org/10.1002/ccr3.727 |
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