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Successful outcome of three patients with sickle‐cell disease and fat embolism syndrome treated with intensive exchange transfusion

Fat embolism syndrome (FES) is a rare complication of sickle‐cell disease (SCD) associated with extremely high mortality rates. It affects predominantly non‐SS patients and those with previously mild disease. Rapid institution of exchange transfusion with an aim to reduce HbS to very low levels as s...

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Autores principales: Greaves, Paul, Mathew, Vivek, Peters, Catherine, Rowe, Susan, Amos, Roger J., Tsitsikas, Dimitris A.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: John Wiley and Sons Inc. 2016
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5224784/
https://www.ncbi.nlm.nih.gov/pubmed/28096988
http://dx.doi.org/10.1002/ccr3.727
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author Greaves, Paul
Mathew, Vivek
Peters, Catherine
Rowe, Susan
Amos, Roger J.
Tsitsikas, Dimitris A.
author_facet Greaves, Paul
Mathew, Vivek
Peters, Catherine
Rowe, Susan
Amos, Roger J.
Tsitsikas, Dimitris A.
author_sort Greaves, Paul
collection PubMed
description Fat embolism syndrome (FES) is a rare complication of sickle‐cell disease (SCD) associated with extremely high mortality rates. It affects predominantly non‐SS patients and those with previously mild disease. Rapid institution of exchange transfusion with an aim to reduce HbS to very low levels as soon as FES is suspected can be life‐saving.
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spelling pubmed-52247842017-01-17 Successful outcome of three patients with sickle‐cell disease and fat embolism syndrome treated with intensive exchange transfusion Greaves, Paul Mathew, Vivek Peters, Catherine Rowe, Susan Amos, Roger J. Tsitsikas, Dimitris A. Clin Case Rep Case Reports Fat embolism syndrome (FES) is a rare complication of sickle‐cell disease (SCD) associated with extremely high mortality rates. It affects predominantly non‐SS patients and those with previously mild disease. Rapid institution of exchange transfusion with an aim to reduce HbS to very low levels as soon as FES is suspected can be life‐saving. John Wiley and Sons Inc. 2016-12-20 /pmc/articles/PMC5224784/ /pubmed/28096988 http://dx.doi.org/10.1002/ccr3.727 Text en © 2016 The Authors. Clinical Case Reports published by John Wiley & Sons Ltd. This is an open access article under the terms of the Creative Commons Attribution‐NonCommercial‐NoDerivs (http://creativecommons.org/licenses/by-nc-nd/4.0/) License, which permits use and distribution in any medium, provided the original work is properly cited, the use is non‐commercial and no modifications or adaptations are made.
spellingShingle Case Reports
Greaves, Paul
Mathew, Vivek
Peters, Catherine
Rowe, Susan
Amos, Roger J.
Tsitsikas, Dimitris A.
Successful outcome of three patients with sickle‐cell disease and fat embolism syndrome treated with intensive exchange transfusion
title Successful outcome of three patients with sickle‐cell disease and fat embolism syndrome treated with intensive exchange transfusion
title_full Successful outcome of three patients with sickle‐cell disease and fat embolism syndrome treated with intensive exchange transfusion
title_fullStr Successful outcome of three patients with sickle‐cell disease and fat embolism syndrome treated with intensive exchange transfusion
title_full_unstemmed Successful outcome of three patients with sickle‐cell disease and fat embolism syndrome treated with intensive exchange transfusion
title_short Successful outcome of three patients with sickle‐cell disease and fat embolism syndrome treated with intensive exchange transfusion
title_sort successful outcome of three patients with sickle‐cell disease and fat embolism syndrome treated with intensive exchange transfusion
topic Case Reports
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5224784/
https://www.ncbi.nlm.nih.gov/pubmed/28096988
http://dx.doi.org/10.1002/ccr3.727
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