A case of proteinase 3 anti-neutrophil cytoplasmic antibody (PR3-ANCA) positive/IgG4-related lung disease

IgG4-related lung disease (IgG4-RLD) is a rare and chronic progressive autoimmune disease. We report a case of IgG4-related inflammatory pseudo-tumor of the lung that was seropositive for proteinase 3 anti-neutrophil cytoplasmic antibody (PR3-ANCA). A 61-year-old male had a mass lesion in the right...

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Detalles Bibliográficos
Autores principales: Touge, Hirokazu, Tomita, Katsuyuki, Yamasaki, Akira, Shimizu, Eiji
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2017
Materias:
Article
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5239823/
https://www.ncbi.nlm.nih.gov/pubmed/28119817
http://dx.doi.org/10.1016/j.rmcr.2017.01.001
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author Touge, Hirokazu
Tomita, Katsuyuki
Yamasaki, Akira
Shimizu, Eiji
author_facet Touge, Hirokazu
Tomita, Katsuyuki
Yamasaki, Akira
Shimizu, Eiji
author_sort Touge, Hirokazu
collection PubMed
description IgG4-related lung disease (IgG4-RLD) is a rare and chronic progressive autoimmune disease. We report a case of IgG4-related inflammatory pseudo-tumor of the lung that was seropositive for proteinase 3 anti-neutrophil cytoplasmic antibody (PR3-ANCA). A 61-year-old male had a mass lesion in the right lower lung field in chest X-ray. Transbronchial lung biopsy resulted in a pathological diagnosis of IgG4-RLD. The condition was improved by hormonal therapy.
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spelling pubmed-52398232017-01-24 A case of proteinase 3 anti-neutrophil cytoplasmic antibody (PR3-ANCA) positive/IgG4-related lung disease Touge, Hirokazu Tomita, Katsuyuki Yamasaki, Akira Shimizu, Eiji Respir Med Case Rep Article IgG4-related lung disease (IgG4-RLD) is a rare and chronic progressive autoimmune disease. We report a case of IgG4-related inflammatory pseudo-tumor of the lung that was seropositive for proteinase 3 anti-neutrophil cytoplasmic antibody (PR3-ANCA). A 61-year-old male had a mass lesion in the right lower lung field in chest X-ray. Transbronchial lung biopsy resulted in a pathological diagnosis of IgG4-RLD. The condition was improved by hormonal therapy. Elsevier 2017-01-06 /pmc/articles/PMC5239823/ /pubmed/28119817 http://dx.doi.org/10.1016/j.rmcr.2017.01.001 Text en © 2017 The Authors http://creativecommons.org/licenses/by-nc-nd/4.0/ This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/).
spellingShingle Article
Touge, Hirokazu
Tomita, Katsuyuki
Yamasaki, Akira
Shimizu, Eiji
A case of proteinase 3 anti-neutrophil cytoplasmic antibody (PR3-ANCA) positive/IgG4-related lung disease
title A case of proteinase 3 anti-neutrophil cytoplasmic antibody (PR3-ANCA) positive/IgG4-related lung disease
title_full A case of proteinase 3 anti-neutrophil cytoplasmic antibody (PR3-ANCA) positive/IgG4-related lung disease
title_fullStr A case of proteinase 3 anti-neutrophil cytoplasmic antibody (PR3-ANCA) positive/IgG4-related lung disease
title_full_unstemmed A case of proteinase 3 anti-neutrophil cytoplasmic antibody (PR3-ANCA) positive/IgG4-related lung disease
title_short A case of proteinase 3 anti-neutrophil cytoplasmic antibody (PR3-ANCA) positive/IgG4-related lung disease
title_sort case of proteinase 3 anti-neutrophil cytoplasmic antibody (pr3-anca) positive/igg4-related lung disease
topic Article
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5239823/
https://www.ncbi.nlm.nih.gov/pubmed/28119817
http://dx.doi.org/10.1016/j.rmcr.2017.01.001
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