Recurrent ovarian Sertoli–Leydig cell tumor in a child with Peutz–Jeghers syndrome

We present a female child with Peutz–Jeghers syndrome (PJS) with a recurrent ovarian Sertoli–Leydig cell tumor (SLCT). SLCTs are relatively rare sex cord neoplasms that can occur in PJS. The patient was an African-American female who first presented at the age of 3 years with precocious puberty, and...

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Autores principales: Bellfield, Edward J., Alemzadeh, Ramin
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Oxford University Press 2016
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5242372/
https://www.ncbi.nlm.nih.gov/pubmed/28101370
http://dx.doi.org/10.1093/omcr/omw048
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author Bellfield, Edward J.
Alemzadeh, Ramin
author_facet Bellfield, Edward J.
Alemzadeh, Ramin
author_sort Bellfield, Edward J.
collection PubMed
description We present a female child with Peutz–Jeghers syndrome (PJS) with a recurrent ovarian Sertoli–Leydig cell tumor (SLCT). SLCTs are relatively rare sex cord neoplasms that can occur in PJS. The patient was an African-American female who first presented at the age of 3 years with precocious puberty, and then at the age of 17 years with abdominal pain and irregular menses. In each case, she had resection of the mass, which included oophorectomy. To our knowledge, this is the first reported case in a child with PJS to have a recurrent ovarian SLCT.
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spelling pubmed-52423722017-01-18 Recurrent ovarian Sertoli–Leydig cell tumor in a child with Peutz–Jeghers syndrome Bellfield, Edward J. Alemzadeh, Ramin Oxf Med Case Reports Case Report We present a female child with Peutz–Jeghers syndrome (PJS) with a recurrent ovarian Sertoli–Leydig cell tumor (SLCT). SLCTs are relatively rare sex cord neoplasms that can occur in PJS. The patient was an African-American female who first presented at the age of 3 years with precocious puberty, and then at the age of 17 years with abdominal pain and irregular menses. In each case, she had resection of the mass, which included oophorectomy. To our knowledge, this is the first reported case in a child with PJS to have a recurrent ovarian SLCT. Oxford University Press 2016-08-29 /pmc/articles/PMC5242372/ /pubmed/28101370 http://dx.doi.org/10.1093/omcr/omw048 Text en © The Author 2016. Published by Oxford University Press. http://creativecommons.org/licenses/by-nc/4.0/ This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/4.0/), which permits non-commercial re-use, distribution, and reproduction in any medium, provided the original work is properly cited. For commercial re-use, please contact journals.permissions@oup.com
spellingShingle Case Report
Bellfield, Edward J.
Alemzadeh, Ramin
Recurrent ovarian Sertoli–Leydig cell tumor in a child with Peutz–Jeghers syndrome
title Recurrent ovarian Sertoli–Leydig cell tumor in a child with Peutz–Jeghers syndrome
title_full Recurrent ovarian Sertoli–Leydig cell tumor in a child with Peutz–Jeghers syndrome
title_fullStr Recurrent ovarian Sertoli–Leydig cell tumor in a child with Peutz–Jeghers syndrome
title_full_unstemmed Recurrent ovarian Sertoli–Leydig cell tumor in a child with Peutz–Jeghers syndrome
title_short Recurrent ovarian Sertoli–Leydig cell tumor in a child with Peutz–Jeghers syndrome
title_sort recurrent ovarian sertoli–leydig cell tumor in a child with peutz–jeghers syndrome
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5242372/
https://www.ncbi.nlm.nih.gov/pubmed/28101370
http://dx.doi.org/10.1093/omcr/omw048
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