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Atteinte hépatique au cours de la maladie de Rendu-Osler: à propos d’un cas et revue de la littérature

A 48 years-old-woman was admitted for anectric cholestasis. A history of recurrent personal and familial epistaxis was noted. Biologic findings revealed iron deficiency anemia and moderate cholestasis. Viral serologic tests, antimitochondrie and anti smooth muscle antibodies were negative. Abdominal...

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Detalles Bibliográficos
Autores principales: Loukil, Hanen, Snoussi, Mouna, Fourati, Hela, Frikha, Faten, Salah, Raida Ben, Jallouli, Moez, Marzouk, Sameh, Mnif, Zeineb, Bahloul, Zouhir
Formato: Online Artículo Texto
Lenguaje:English
Publicado: The African Field Epidemiology Network 2016
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5267911/
https://www.ncbi.nlm.nih.gov/pubmed/28154681
http://dx.doi.org/10.11604/pamj.2016.24.326.9816
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author Loukil, Hanen
Snoussi, Mouna
Fourati, Hela
Frikha, Faten
Salah, Raida Ben
Jallouli, Moez
Marzouk, Sameh
Mnif, Zeineb
Bahloul, Zouhir
author_facet Loukil, Hanen
Snoussi, Mouna
Fourati, Hela
Frikha, Faten
Salah, Raida Ben
Jallouli, Moez
Marzouk, Sameh
Mnif, Zeineb
Bahloul, Zouhir
author_sort Loukil, Hanen
collection PubMed
description A 48 years-old-woman was admitted for anectric cholestasis. A history of recurrent personal and familial epistaxis was noted. Biologic findings revealed iron deficiency anemia and moderate cholestasis. Viral serologic tests, antimitochondrie and anti smooth muscle antibodies were negative. Abdominal tomography showed multiple arterio-venous shunts of the liver. The diagnosis of liver involvement due to Rendu Osler disease was made. Treatment with oral ferrous iron of 150 mg/day was administered and regular biological and morphologic controls of liver was decided.
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spelling pubmed-52679112017-02-02 Atteinte hépatique au cours de la maladie de Rendu-Osler: à propos d’un cas et revue de la littérature Loukil, Hanen Snoussi, Mouna Fourati, Hela Frikha, Faten Salah, Raida Ben Jallouli, Moez Marzouk, Sameh Mnif, Zeineb Bahloul, Zouhir Pan Afr Med J Case Report A 48 years-old-woman was admitted for anectric cholestasis. A history of recurrent personal and familial epistaxis was noted. Biologic findings revealed iron deficiency anemia and moderate cholestasis. Viral serologic tests, antimitochondrie and anti smooth muscle antibodies were negative. Abdominal tomography showed multiple arterio-venous shunts of the liver. The diagnosis of liver involvement due to Rendu Osler disease was made. Treatment with oral ferrous iron of 150 mg/day was administered and regular biological and morphologic controls of liver was decided. The African Field Epidemiology Network 2016-08-25 /pmc/articles/PMC5267911/ /pubmed/28154681 http://dx.doi.org/10.11604/pamj.2016.24.326.9816 Text en © Hanen Loukil et al. http://creativecommons.org/licenses/by/2.0/ The Pan African Medical Journal - ISSN 1937-8688. This is an Open Access article distributed under the terms of the Creative Commons Attribution License which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Loukil, Hanen
Snoussi, Mouna
Fourati, Hela
Frikha, Faten
Salah, Raida Ben
Jallouli, Moez
Marzouk, Sameh
Mnif, Zeineb
Bahloul, Zouhir
Atteinte hépatique au cours de la maladie de Rendu-Osler: à propos d’un cas et revue de la littérature
title Atteinte hépatique au cours de la maladie de Rendu-Osler: à propos d’un cas et revue de la littérature
title_full Atteinte hépatique au cours de la maladie de Rendu-Osler: à propos d’un cas et revue de la littérature
title_fullStr Atteinte hépatique au cours de la maladie de Rendu-Osler: à propos d’un cas et revue de la littérature
title_full_unstemmed Atteinte hépatique au cours de la maladie de Rendu-Osler: à propos d’un cas et revue de la littérature
title_short Atteinte hépatique au cours de la maladie de Rendu-Osler: à propos d’un cas et revue de la littérature
title_sort atteinte hépatique au cours de la maladie de rendu-osler: à propos d’un cas et revue de la littérature
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5267911/
https://www.ncbi.nlm.nih.gov/pubmed/28154681
http://dx.doi.org/10.11604/pamj.2016.24.326.9816
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