Atypical Teratoid/Rhabdoid Tumor of the Sellar Region in an Adult With Long Survival: Case Report and Review of the Literature

Atypical teratoid/rhabdoid tumor (AT/RT) is a highly malignant central nervous system neoplasm usually diagnosed in young children, although it can occur in adults. Prognosis for AT/RT is poor, with a median survival of 10 - 11 months. We report a rare case of adult sellar and suprasellar AT/RT in a...

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Autores principales: Almalki, Mussa Hussain, Alrogi, Ashjan, Al-Rabie, Abdulkarim, Al-Dandan, Sadeq, Altwairgi, Abdullah, Orz, Yasser
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elmer Press 2017
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5289142/
https://www.ncbi.nlm.nih.gov/pubmed/28179970
http://dx.doi.org/10.14740/jocmr2922w
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author Almalki, Mussa Hussain
Alrogi, Ashjan
Al-Rabie, Abdulkarim
Al-Dandan, Sadeq
Altwairgi, Abdullah
Orz, Yasser
author_facet Almalki, Mussa Hussain
Alrogi, Ashjan
Al-Rabie, Abdulkarim
Al-Dandan, Sadeq
Altwairgi, Abdullah
Orz, Yasser
author_sort Almalki, Mussa Hussain
collection PubMed
description Atypical teratoid/rhabdoid tumor (AT/RT) is a highly malignant central nervous system neoplasm usually diagnosed in young children, although it can occur in adults. Prognosis for AT/RT is poor, with a median survival of 10 - 11 months. We report a rare case of adult sellar and suprasellar AT/RT in a 36-year-old female patient. She was treated with multi-modalities including surgery, chemotherapy and radiation. She markedly improved following treatment with no recurrence in 3 years follow-up. To our knowledge, this is the 11th case of an adult-onset AT/RT in the sellar or suprasellar region with favorable long-term outcome.
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spelling pubmed-52891422017-02-08 Atypical Teratoid/Rhabdoid Tumor of the Sellar Region in an Adult With Long Survival: Case Report and Review of the Literature Almalki, Mussa Hussain Alrogi, Ashjan Al-Rabie, Abdulkarim Al-Dandan, Sadeq Altwairgi, Abdullah Orz, Yasser J Clin Med Res Case Report Atypical teratoid/rhabdoid tumor (AT/RT) is a highly malignant central nervous system neoplasm usually diagnosed in young children, although it can occur in adults. Prognosis for AT/RT is poor, with a median survival of 10 - 11 months. We report a rare case of adult sellar and suprasellar AT/RT in a 36-year-old female patient. She was treated with multi-modalities including surgery, chemotherapy and radiation. She markedly improved following treatment with no recurrence in 3 years follow-up. To our knowledge, this is the 11th case of an adult-onset AT/RT in the sellar or suprasellar region with favorable long-term outcome. Elmer Press 2017-03 2017-01-25 /pmc/articles/PMC5289142/ /pubmed/28179970 http://dx.doi.org/10.14740/jocmr2922w Text en Copyright 2017, Almalki et al. http://creativecommons.org/licenses/by-nc/4.0/ This article is distributed under the terms of the Creative Commons Attribution Non-Commercial 4.0 International License, which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Almalki, Mussa Hussain
Alrogi, Ashjan
Al-Rabie, Abdulkarim
Al-Dandan, Sadeq
Altwairgi, Abdullah
Orz, Yasser
Atypical Teratoid/Rhabdoid Tumor of the Sellar Region in an Adult With Long Survival: Case Report and Review of the Literature
title Atypical Teratoid/Rhabdoid Tumor of the Sellar Region in an Adult With Long Survival: Case Report and Review of the Literature
title_full Atypical Teratoid/Rhabdoid Tumor of the Sellar Region in an Adult With Long Survival: Case Report and Review of the Literature
title_fullStr Atypical Teratoid/Rhabdoid Tumor of the Sellar Region in an Adult With Long Survival: Case Report and Review of the Literature
title_full_unstemmed Atypical Teratoid/Rhabdoid Tumor of the Sellar Region in an Adult With Long Survival: Case Report and Review of the Literature
title_short Atypical Teratoid/Rhabdoid Tumor of the Sellar Region in an Adult With Long Survival: Case Report and Review of the Literature
title_sort atypical teratoid/rhabdoid tumor of the sellar region in an adult with long survival: case report and review of the literature
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5289142/
https://www.ncbi.nlm.nih.gov/pubmed/28179970
http://dx.doi.org/10.14740/jocmr2922w
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