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Acute bulbar palsy plus syndrome: A rare variant of Guillain–Barre syndrome
Guillain–Barre syndrome (GBS) is the most common cause of acute flaccid paralysis worldwide both in adult and pediatric population. Although flaccid paralysis is the hallmark of this disease, there are some rare variants which may be easily missed unless suspected. Here, we present a very rare varia...
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Formato: | Online Artículo Texto |
Lenguaje: | English |
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Medknow Publications & Media Pvt Ltd
2016
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Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5314846/ https://www.ncbi.nlm.nih.gov/pubmed/28217155 http://dx.doi.org/10.4103/1817-1745.199480 |
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author | Ray, Sanghamitra Jain, Prakash Chand |
author_facet | Ray, Sanghamitra Jain, Prakash Chand |
author_sort | Ray, Sanghamitra |
collection | PubMed |
description | Guillain–Barre syndrome (GBS) is the most common cause of acute flaccid paralysis worldwide both in adult and pediatric population. Although flaccid paralysis is the hallmark of this disease, there are some rare variants which may be easily missed unless suspected. Here, we present a very rare variant of GBS - acute bulbar palsy plus syndrome in a pediatric patient. A 13-year-old female child presented with right-sided lower motor neuron type of facial palsy and palsy of bilateral glossopharyngeal and vagus nerve of 2 weeks duration. On detailed neurological examination, motor and sensory system were normal, but the deep tendon reflexes were absent universally. Nerve conduction study showed demyelinating motor neuropathy. Based on typical clinical course and electrophysiological studies, the diagnosis was made. To the best of our knowledge, this is the first pediatric case of unilateral facial palsy with bulbar involvement without any motor abnormality. |
format | Online Article Text |
id | pubmed-5314846 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2016 |
publisher | Medknow Publications & Media Pvt Ltd |
record_format | MEDLINE/PubMed |
spelling | pubmed-53148462017-02-17 Acute bulbar palsy plus syndrome: A rare variant of Guillain–Barre syndrome Ray, Sanghamitra Jain, Prakash Chand J Pediatr Neurosci Case Report Guillain–Barre syndrome (GBS) is the most common cause of acute flaccid paralysis worldwide both in adult and pediatric population. Although flaccid paralysis is the hallmark of this disease, there are some rare variants which may be easily missed unless suspected. Here, we present a very rare variant of GBS - acute bulbar palsy plus syndrome in a pediatric patient. A 13-year-old female child presented with right-sided lower motor neuron type of facial palsy and palsy of bilateral glossopharyngeal and vagus nerve of 2 weeks duration. On detailed neurological examination, motor and sensory system were normal, but the deep tendon reflexes were absent universally. Nerve conduction study showed demyelinating motor neuropathy. Based on typical clinical course and electrophysiological studies, the diagnosis was made. To the best of our knowledge, this is the first pediatric case of unilateral facial palsy with bulbar involvement without any motor abnormality. Medknow Publications & Media Pvt Ltd 2016 /pmc/articles/PMC5314846/ /pubmed/28217155 http://dx.doi.org/10.4103/1817-1745.199480 Text en Copyright: © 2017 Journal of Pediatric Neurosciences http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open access article distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 3.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as the author is credited and the new creations are licensed under the identical terms. |
spellingShingle | Case Report Ray, Sanghamitra Jain, Prakash Chand Acute bulbar palsy plus syndrome: A rare variant of Guillain–Barre syndrome |
title | Acute bulbar palsy plus syndrome: A rare variant of Guillain–Barre syndrome |
title_full | Acute bulbar palsy plus syndrome: A rare variant of Guillain–Barre syndrome |
title_fullStr | Acute bulbar palsy plus syndrome: A rare variant of Guillain–Barre syndrome |
title_full_unstemmed | Acute bulbar palsy plus syndrome: A rare variant of Guillain–Barre syndrome |
title_short | Acute bulbar palsy plus syndrome: A rare variant of Guillain–Barre syndrome |
title_sort | acute bulbar palsy plus syndrome: a rare variant of guillain–barre syndrome |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5314846/ https://www.ncbi.nlm.nih.gov/pubmed/28217155 http://dx.doi.org/10.4103/1817-1745.199480 |
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