Cargando…

Acute bulbar palsy plus syndrome: A rare variant of Guillain–Barre syndrome

Guillain–Barre syndrome (GBS) is the most common cause of acute flaccid paralysis worldwide both in adult and pediatric population. Although flaccid paralysis is the hallmark of this disease, there are some rare variants which may be easily missed unless suspected. Here, we present a very rare varia...

Descripción completa

Detalles Bibliográficos
Autores principales: Ray, Sanghamitra, Jain, Prakash Chand
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2016
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5314846/
https://www.ncbi.nlm.nih.gov/pubmed/28217155
http://dx.doi.org/10.4103/1817-1745.199480
_version_ 1782508595009552384
author Ray, Sanghamitra
Jain, Prakash Chand
author_facet Ray, Sanghamitra
Jain, Prakash Chand
author_sort Ray, Sanghamitra
collection PubMed
description Guillain–Barre syndrome (GBS) is the most common cause of acute flaccid paralysis worldwide both in adult and pediatric population. Although flaccid paralysis is the hallmark of this disease, there are some rare variants which may be easily missed unless suspected. Here, we present a very rare variant of GBS - acute bulbar palsy plus syndrome in a pediatric patient. A 13-year-old female child presented with right-sided lower motor neuron type of facial palsy and palsy of bilateral glossopharyngeal and vagus nerve of 2 weeks duration. On detailed neurological examination, motor and sensory system were normal, but the deep tendon reflexes were absent universally. Nerve conduction study showed demyelinating motor neuropathy. Based on typical clinical course and electrophysiological studies, the diagnosis was made. To the best of our knowledge, this is the first pediatric case of unilateral facial palsy with bulbar involvement without any motor abnormality.
format Online
Article
Text
id pubmed-5314846
institution National Center for Biotechnology Information
language English
publishDate 2016
publisher Medknow Publications & Media Pvt Ltd
record_format MEDLINE/PubMed
spelling pubmed-53148462017-02-17 Acute bulbar palsy plus syndrome: A rare variant of Guillain–Barre syndrome Ray, Sanghamitra Jain, Prakash Chand J Pediatr Neurosci Case Report Guillain–Barre syndrome (GBS) is the most common cause of acute flaccid paralysis worldwide both in adult and pediatric population. Although flaccid paralysis is the hallmark of this disease, there are some rare variants which may be easily missed unless suspected. Here, we present a very rare variant of GBS - acute bulbar palsy plus syndrome in a pediatric patient. A 13-year-old female child presented with right-sided lower motor neuron type of facial palsy and palsy of bilateral glossopharyngeal and vagus nerve of 2 weeks duration. On detailed neurological examination, motor and sensory system were normal, but the deep tendon reflexes were absent universally. Nerve conduction study showed demyelinating motor neuropathy. Based on typical clinical course and electrophysiological studies, the diagnosis was made. To the best of our knowledge, this is the first pediatric case of unilateral facial palsy with bulbar involvement without any motor abnormality. Medknow Publications & Media Pvt Ltd 2016 /pmc/articles/PMC5314846/ /pubmed/28217155 http://dx.doi.org/10.4103/1817-1745.199480 Text en Copyright: © 2017 Journal of Pediatric Neurosciences http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open access article distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 3.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as the author is credited and the new creations are licensed under the identical terms.
spellingShingle Case Report
Ray, Sanghamitra
Jain, Prakash Chand
Acute bulbar palsy plus syndrome: A rare variant of Guillain–Barre syndrome
title Acute bulbar palsy plus syndrome: A rare variant of Guillain–Barre syndrome
title_full Acute bulbar palsy plus syndrome: A rare variant of Guillain–Barre syndrome
title_fullStr Acute bulbar palsy plus syndrome: A rare variant of Guillain–Barre syndrome
title_full_unstemmed Acute bulbar palsy plus syndrome: A rare variant of Guillain–Barre syndrome
title_short Acute bulbar palsy plus syndrome: A rare variant of Guillain–Barre syndrome
title_sort acute bulbar palsy plus syndrome: a rare variant of guillain–barre syndrome
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5314846/
https://www.ncbi.nlm.nih.gov/pubmed/28217155
http://dx.doi.org/10.4103/1817-1745.199480
work_keys_str_mv AT raysanghamitra acutebulbarpalsyplussyndromeararevariantofguillainbarresyndrome
AT jainprakashchand acutebulbarpalsyplussyndromeararevariantofguillainbarresyndrome