Cargando…

Functional hemispherotomy in Rasmussen syndrome in the absence of classic MRI findings

A 7-year-old previously healthy girl presented with a left-sided focal seizure without impaired consciousness and subsequently developed epilepsia partialis continua. Initial MRI was normal, and the subsequent images only showed a focal T2/FLAIR hyperintense area without cortical atrophy. She was di...

Descripción completa

Detalles Bibliográficos
Autores principales: Nagahama, Yasunori, Joshi, Charuta, Dlouhy, Brian, Wu, Angela Y., Abel, Taylor J., Baumbach, Gary, Kawasaki, Hiroto
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2016
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5315437/
https://www.ncbi.nlm.nih.gov/pubmed/28239546
http://dx.doi.org/10.1016/j.ebcr.2016.11.003
Descripción
Sumario:A 7-year-old previously healthy girl presented with a left-sided focal seizure without impaired consciousness and subsequently developed epilepsia partialis continua. Initial MRI was normal, and the subsequent images only showed a focal T2/FLAIR hyperintense area without cortical atrophy. She was diagnosed with Rasmussen syndrome by pathology and promptly treated with functional hemispherotomy. Rasmussen syndrome is a rare progressive neurological disorder, the only definitive cure for which is hemispheric disconnection. The disease presents a management dilemma, especially early in disease course without characteristic neuroimaging features. A high index of suspicion, multidisciplinary approach, and clear timely communication with the family are critical.