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Functional hemispherotomy in Rasmussen syndrome in the absence of classic MRI findings

A 7-year-old previously healthy girl presented with a left-sided focal seizure without impaired consciousness and subsequently developed epilepsia partialis continua. Initial MRI was normal, and the subsequent images only showed a focal T2/FLAIR hyperintense area without cortical atrophy. She was di...

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Autores principales: Nagahama, Yasunori, Joshi, Charuta, Dlouhy, Brian, Wu, Angela Y., Abel, Taylor J., Baumbach, Gary, Kawasaki, Hiroto
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2016
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5315437/
https://www.ncbi.nlm.nih.gov/pubmed/28239546
http://dx.doi.org/10.1016/j.ebcr.2016.11.003
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author Nagahama, Yasunori
Joshi, Charuta
Dlouhy, Brian
Wu, Angela Y.
Abel, Taylor J.
Baumbach, Gary
Kawasaki, Hiroto
author_facet Nagahama, Yasunori
Joshi, Charuta
Dlouhy, Brian
Wu, Angela Y.
Abel, Taylor J.
Baumbach, Gary
Kawasaki, Hiroto
author_sort Nagahama, Yasunori
collection PubMed
description A 7-year-old previously healthy girl presented with a left-sided focal seizure without impaired consciousness and subsequently developed epilepsia partialis continua. Initial MRI was normal, and the subsequent images only showed a focal T2/FLAIR hyperintense area without cortical atrophy. She was diagnosed with Rasmussen syndrome by pathology and promptly treated with functional hemispherotomy. Rasmussen syndrome is a rare progressive neurological disorder, the only definitive cure for which is hemispheric disconnection. The disease presents a management dilemma, especially early in disease course without characteristic neuroimaging features. A high index of suspicion, multidisciplinary approach, and clear timely communication with the family are critical.
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spelling pubmed-53154372017-02-26 Functional hemispherotomy in Rasmussen syndrome in the absence of classic MRI findings Nagahama, Yasunori Joshi, Charuta Dlouhy, Brian Wu, Angela Y. Abel, Taylor J. Baumbach, Gary Kawasaki, Hiroto Epilepsy Behav Case Rep Case Report A 7-year-old previously healthy girl presented with a left-sided focal seizure without impaired consciousness and subsequently developed epilepsia partialis continua. Initial MRI was normal, and the subsequent images only showed a focal T2/FLAIR hyperintense area without cortical atrophy. She was diagnosed with Rasmussen syndrome by pathology and promptly treated with functional hemispherotomy. Rasmussen syndrome is a rare progressive neurological disorder, the only definitive cure for which is hemispheric disconnection. The disease presents a management dilemma, especially early in disease course without characteristic neuroimaging features. A high index of suspicion, multidisciplinary approach, and clear timely communication with the family are critical. Elsevier 2016-12-05 /pmc/articles/PMC5315437/ /pubmed/28239546 http://dx.doi.org/10.1016/j.ebcr.2016.11.003 Text en © 2016 The Authors http://creativecommons.org/licenses/by-nc-nd/4.0/ This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/).
spellingShingle Case Report
Nagahama, Yasunori
Joshi, Charuta
Dlouhy, Brian
Wu, Angela Y.
Abel, Taylor J.
Baumbach, Gary
Kawasaki, Hiroto
Functional hemispherotomy in Rasmussen syndrome in the absence of classic MRI findings
title Functional hemispherotomy in Rasmussen syndrome in the absence of classic MRI findings
title_full Functional hemispherotomy in Rasmussen syndrome in the absence of classic MRI findings
title_fullStr Functional hemispherotomy in Rasmussen syndrome in the absence of classic MRI findings
title_full_unstemmed Functional hemispherotomy in Rasmussen syndrome in the absence of classic MRI findings
title_short Functional hemispherotomy in Rasmussen syndrome in the absence of classic MRI findings
title_sort functional hemispherotomy in rasmussen syndrome in the absence of classic mri findings
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5315437/
https://www.ncbi.nlm.nih.gov/pubmed/28239546
http://dx.doi.org/10.1016/j.ebcr.2016.11.003
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