Cargando…
Steatocystoma multiplex suppurativa: case report of a rare condition
Steatocystoma multiplex is a rare genetic disorder characterized by the presence of hamartomatous malformations at the junction of the pilosebaceous duct. It consists of encapsulated cystic lesions in the dermis, with adjacent sebaceous gland. When associated with inflammation, resembling hidradenit...
Autores principales: | , , , , , |
---|---|
Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Sociedade Brasileira de Dermatologia
2016
|
Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5324992/ https://www.ncbi.nlm.nih.gov/pubmed/28300893 http://dx.doi.org/10.1590/abd1806-4841.20164539 |
_version_ | 1782510302231789568 |
---|---|
author | Santana, Cândida Naira Lima e Lima Pereira, Daniele do Nascimento Lisboa, Alice Paixão Leal, Juliana Martins Obadia, Daniel Lago da Silva, Roberto Souto |
author_facet | Santana, Cândida Naira Lima e Lima Pereira, Daniele do Nascimento Lisboa, Alice Paixão Leal, Juliana Martins Obadia, Daniel Lago da Silva, Roberto Souto |
author_sort | Santana, Cândida Naira Lima e Lima |
collection | PubMed |
description | Steatocystoma multiplex is a rare genetic disorder characterized by the presence of hamartomatous malformations at the junction of the pilosebaceous duct. It consists of encapsulated cystic lesions in the dermis, with adjacent sebaceous gland. When associated with inflammation, resembling hidradenitis, it is called steatocystoma multiplex suppurativa, a condition rarely reported. This is the first case of steatocystoma multiplex suppurativa reported in the Brazilian literature. Female patient, 23 years old, with papular and nodular cystic lesions that started in the armpits and groin, later spreading to the trunk, lower limbs, anticubital fossa, face and scalp. The presence of papular-nodular lesions associated with disseminated hidradenitis-like lesions in flexural areas and the histopathological diagnosis of steatocystoma defined the diagnosis of steatocystoma multiplex suppurativa. |
format | Online Article Text |
id | pubmed-5324992 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2016 |
publisher | Sociedade Brasileira de Dermatologia |
record_format | MEDLINE/PubMed |
spelling | pubmed-53249922017-03-02 Steatocystoma multiplex suppurativa: case report of a rare condition Santana, Cândida Naira Lima e Lima Pereira, Daniele do Nascimento Lisboa, Alice Paixão Leal, Juliana Martins Obadia, Daniel Lago da Silva, Roberto Souto An Bras Dermatol Case Report Steatocystoma multiplex is a rare genetic disorder characterized by the presence of hamartomatous malformations at the junction of the pilosebaceous duct. It consists of encapsulated cystic lesions in the dermis, with adjacent sebaceous gland. When associated with inflammation, resembling hidradenitis, it is called steatocystoma multiplex suppurativa, a condition rarely reported. This is the first case of steatocystoma multiplex suppurativa reported in the Brazilian literature. Female patient, 23 years old, with papular and nodular cystic lesions that started in the armpits and groin, later spreading to the trunk, lower limbs, anticubital fossa, face and scalp. The presence of papular-nodular lesions associated with disseminated hidradenitis-like lesions in flexural areas and the histopathological diagnosis of steatocystoma defined the diagnosis of steatocystoma multiplex suppurativa. Sociedade Brasileira de Dermatologia 2016 /pmc/articles/PMC5324992/ /pubmed/28300893 http://dx.doi.org/10.1590/abd1806-4841.20164539 Text en http://creativecommons.org/licenses/by/4.0/ This is an Open Access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited. |
spellingShingle | Case Report Santana, Cândida Naira Lima e Lima Pereira, Daniele do Nascimento Lisboa, Alice Paixão Leal, Juliana Martins Obadia, Daniel Lago da Silva, Roberto Souto Steatocystoma multiplex suppurativa: case report of a rare condition |
title | Steatocystoma multiplex suppurativa: case report of a rare
condition |
title_full | Steatocystoma multiplex suppurativa: case report of a rare
condition |
title_fullStr | Steatocystoma multiplex suppurativa: case report of a rare
condition |
title_full_unstemmed | Steatocystoma multiplex suppurativa: case report of a rare
condition |
title_short | Steatocystoma multiplex suppurativa: case report of a rare
condition |
title_sort | steatocystoma multiplex suppurativa: case report of a rare
condition |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5324992/ https://www.ncbi.nlm.nih.gov/pubmed/28300893 http://dx.doi.org/10.1590/abd1806-4841.20164539 |
work_keys_str_mv | AT santanacandidanairalimaelima steatocystomamultiplexsuppurativacasereportofararecondition AT pereiradanieledonascimento steatocystomamultiplexsuppurativacasereportofararecondition AT lisboaalicepaixao steatocystomamultiplexsuppurativacasereportofararecondition AT lealjulianamartins steatocystomamultiplexsuppurativacasereportofararecondition AT obadiadaniellago steatocystomamultiplexsuppurativacasereportofararecondition AT dasilvarobertosouto steatocystomamultiplexsuppurativacasereportofararecondition |