Hemoglobin Kansas as a Rare Cause of Cyanosis: A Case Report and Review of the Literature

Hemoglobin (Hb) Kansas is an inherited Hb variant with a low oxygen affinity that is associated with low oxygen saturation on pulse oximetry (SpO(2)). It leads to asymptomatic cyanosis. Patients with Hb Kansas do not require any specific treatment and the prognosis is good. In patients with unexplai...

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Autores principales: Nagayama, Yoshikuni, Yoshida, Minoru, Kohyama, Tadashi, Matsui, Katsuyuki
Formato: Online Artículo Texto
Lenguaje:English
Publicado: The Japanese Society of Internal Medicine 2017
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5337469/
https://www.ncbi.nlm.nih.gov/pubmed/28090054
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author Nagayama, Yoshikuni
Yoshida, Minoru
Kohyama, Tadashi
Matsui, Katsuyuki
author_facet Nagayama, Yoshikuni
Yoshida, Minoru
Kohyama, Tadashi
Matsui, Katsuyuki
author_sort Nagayama, Yoshikuni
collection PubMed
description Hemoglobin (Hb) Kansas is an inherited Hb variant with a low oxygen affinity that is associated with low oxygen saturation on pulse oximetry (SpO(2)). It leads to asymptomatic cyanosis. Patients with Hb Kansas do not require any specific treatment and the prognosis is good. In patients with unexplained cyanosis, we should thus consider Hb variants, including Hb Kansas and avoid unnecessary investigations and managements. We herein report the case of 65-year-old woman with Hb Kansas and review five other cases (three lineages) that have been reported in Japan.
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spelling pubmed-53374692017-03-08 Hemoglobin Kansas as a Rare Cause of Cyanosis: A Case Report and Review of the Literature Nagayama, Yoshikuni Yoshida, Minoru Kohyama, Tadashi Matsui, Katsuyuki Intern Med Case Report Hemoglobin (Hb) Kansas is an inherited Hb variant with a low oxygen affinity that is associated with low oxygen saturation on pulse oximetry (SpO(2)). It leads to asymptomatic cyanosis. Patients with Hb Kansas do not require any specific treatment and the prognosis is good. In patients with unexplained cyanosis, we should thus consider Hb variants, including Hb Kansas and avoid unnecessary investigations and managements. We herein report the case of 65-year-old woman with Hb Kansas and review five other cases (three lineages) that have been reported in Japan. The Japanese Society of Internal Medicine 2017-01-15 /pmc/articles/PMC5337469/ /pubmed/28090054 Text en https://creativecommons.org/licenses/by-nc-nd/4.0/ The Internal Medicine is an Open Access article distributed under the Creative Commons Attribution-NonCommercial-NoDerivatives 4.0 International License. To view the details of this license, please visit (https://creativecommons.org/licenses/by-nc-nd/4.0/).
spellingShingle Case Report
Nagayama, Yoshikuni
Yoshida, Minoru
Kohyama, Tadashi
Matsui, Katsuyuki
Hemoglobin Kansas as a Rare Cause of Cyanosis: A Case Report and Review of the Literature
title Hemoglobin Kansas as a Rare Cause of Cyanosis: A Case Report and Review of the Literature
title_full Hemoglobin Kansas as a Rare Cause of Cyanosis: A Case Report and Review of the Literature
title_fullStr Hemoglobin Kansas as a Rare Cause of Cyanosis: A Case Report and Review of the Literature
title_full_unstemmed Hemoglobin Kansas as a Rare Cause of Cyanosis: A Case Report and Review of the Literature
title_short Hemoglobin Kansas as a Rare Cause of Cyanosis: A Case Report and Review of the Literature
title_sort hemoglobin kansas as a rare cause of cyanosis: a case report and review of the literature
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5337469/
https://www.ncbi.nlm.nih.gov/pubmed/28090054
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