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Skeletal Dysplasias: Growing Therapy for Growing Bones

Skeletal dysplasias represent a large and diverse group of rare conditions affecting collagen and bone. They can be clinically classified based on radiographic and physical features, and many can be further defined at a molecular level (Bonafe et al., 2015). Early diagnosis is critical to proper med...

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Autores principales: Jelin, Angie C., O'Hare, Elizabeth, Blakemore, Karin, Jelin, Eric B., Valle, David, Hoover-Fong, Julie
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Frontiers Media S.A. 2017
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5337493/
https://www.ncbi.nlm.nih.gov/pubmed/28321190
http://dx.doi.org/10.3389/fphar.2017.00079
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author Jelin, Angie C.
O'Hare, Elizabeth
Blakemore, Karin
Jelin, Eric B.
Valle, David
Hoover-Fong, Julie
author_facet Jelin, Angie C.
O'Hare, Elizabeth
Blakemore, Karin
Jelin, Eric B.
Valle, David
Hoover-Fong, Julie
author_sort Jelin, Angie C.
collection PubMed
description Skeletal dysplasias represent a large and diverse group of rare conditions affecting collagen and bone. They can be clinically classified based on radiographic and physical features, and many can be further defined at a molecular level (Bonafe et al., 2015). Early diagnosis is critical to proper medical management including pharmacologic treatment when available. Patients with severe skeletal dysplasias often have small chests with respiratory insufficiency or airway obstruction and require immediate intubation after birth. Thereafter a variety of orthopedic, neurosurgical, pulmonary, otolaryngology interventions may be needed. In terms of definitive treatment for skeletal dysplasias, there are few pharmacotherapeutic options available for the majority of these conditions. We sought to describe therapies that are currently available or under investigation for skeletal dysplasias.
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spelling pubmed-53374932017-03-20 Skeletal Dysplasias: Growing Therapy for Growing Bones Jelin, Angie C. O'Hare, Elizabeth Blakemore, Karin Jelin, Eric B. Valle, David Hoover-Fong, Julie Front Pharmacol Pharmacology Skeletal dysplasias represent a large and diverse group of rare conditions affecting collagen and bone. They can be clinically classified based on radiographic and physical features, and many can be further defined at a molecular level (Bonafe et al., 2015). Early diagnosis is critical to proper medical management including pharmacologic treatment when available. Patients with severe skeletal dysplasias often have small chests with respiratory insufficiency or airway obstruction and require immediate intubation after birth. Thereafter a variety of orthopedic, neurosurgical, pulmonary, otolaryngology interventions may be needed. In terms of definitive treatment for skeletal dysplasias, there are few pharmacotherapeutic options available for the majority of these conditions. We sought to describe therapies that are currently available or under investigation for skeletal dysplasias. Frontiers Media S.A. 2017-03-06 /pmc/articles/PMC5337493/ /pubmed/28321190 http://dx.doi.org/10.3389/fphar.2017.00079 Text en Copyright © 2017 Jelin, O'Hare, Blakemore, Jelin, Valle and Hoover-Fong. http://creativecommons.org/licenses/by/4.0/ This is an open-access article distributed under the terms of the Creative Commons Attribution License (CC BY). The use, distribution or reproduction in other forums is permitted, provided the original author(s) or licensor are credited and that the original publication in this journal is cited, in accordance with accepted academic practice. No use, distribution or reproduction is permitted which does not comply with these terms.
spellingShingle Pharmacology
Jelin, Angie C.
O'Hare, Elizabeth
Blakemore, Karin
Jelin, Eric B.
Valle, David
Hoover-Fong, Julie
Skeletal Dysplasias: Growing Therapy for Growing Bones
title Skeletal Dysplasias: Growing Therapy for Growing Bones
title_full Skeletal Dysplasias: Growing Therapy for Growing Bones
title_fullStr Skeletal Dysplasias: Growing Therapy for Growing Bones
title_full_unstemmed Skeletal Dysplasias: Growing Therapy for Growing Bones
title_short Skeletal Dysplasias: Growing Therapy for Growing Bones
title_sort skeletal dysplasias: growing therapy for growing bones
topic Pharmacology
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5337493/
https://www.ncbi.nlm.nih.gov/pubmed/28321190
http://dx.doi.org/10.3389/fphar.2017.00079
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