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Anesthetic Implications in a Child with Crouzon Syndrome

Crouzon syndrome (CS) is an autosomal dominant genetic disorder characterized by craniofacial dysostosis. Premature fusion of skull base leads to midfacial hypoplasia, shallow orbit, mandibular prognathism, overcrowding of upper teeth, high-arched palate, and upper airway obstruction. It is importan...

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Autores principales: Kumar, Ajeet, Goel, Nitika, Sinha, Chandni, Singh, Abhishek
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2017
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5341658/
https://www.ncbi.nlm.nih.gov/pubmed/28298794
http://dx.doi.org/10.4103/0259-1162.200234
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author Kumar, Ajeet
Goel, Nitika
Sinha, Chandni
Singh, Abhishek
author_facet Kumar, Ajeet
Goel, Nitika
Sinha, Chandni
Singh, Abhishek
author_sort Kumar, Ajeet
collection PubMed
description Crouzon syndrome (CS) is an autosomal dominant genetic disorder characterized by craniofacial dysostosis. Premature fusion of skull base leads to midfacial hypoplasia, shallow orbit, mandibular prognathism, overcrowding of upper teeth, high-arched palate, and upper airway obstruction. It is important for anesthesiologists managing such patients to recognize and avoid potential airway complications. Here, we present a case of a 10-year-old child with CS posted for ptosis correction surgery. Use of peripheral nerve blocks to cut down opioid requirement, inhalational induction, and maintenance are key aspects in successful management of such cases.
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spelling pubmed-53416582017-03-15 Anesthetic Implications in a Child with Crouzon Syndrome Kumar, Ajeet Goel, Nitika Sinha, Chandni Singh, Abhishek Anesth Essays Res Case Report Crouzon syndrome (CS) is an autosomal dominant genetic disorder characterized by craniofacial dysostosis. Premature fusion of skull base leads to midfacial hypoplasia, shallow orbit, mandibular prognathism, overcrowding of upper teeth, high-arched palate, and upper airway obstruction. It is important for anesthesiologists managing such patients to recognize and avoid potential airway complications. Here, we present a case of a 10-year-old child with CS posted for ptosis correction surgery. Use of peripheral nerve blocks to cut down opioid requirement, inhalational induction, and maintenance are key aspects in successful management of such cases. Medknow Publications & Media Pvt Ltd 2017 /pmc/articles/PMC5341658/ /pubmed/28298794 http://dx.doi.org/10.4103/0259-1162.200234 Text en Copyright: © 2017 Anesthesia: Essays and Researches http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open access article distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 3.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as the author is credited and the new creations are licensed under the identical terms.
spellingShingle Case Report
Kumar, Ajeet
Goel, Nitika
Sinha, Chandni
Singh, Abhishek
Anesthetic Implications in a Child with Crouzon Syndrome
title Anesthetic Implications in a Child with Crouzon Syndrome
title_full Anesthetic Implications in a Child with Crouzon Syndrome
title_fullStr Anesthetic Implications in a Child with Crouzon Syndrome
title_full_unstemmed Anesthetic Implications in a Child with Crouzon Syndrome
title_short Anesthetic Implications in a Child with Crouzon Syndrome
title_sort anesthetic implications in a child with crouzon syndrome
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5341658/
https://www.ncbi.nlm.nih.gov/pubmed/28298794
http://dx.doi.org/10.4103/0259-1162.200234
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