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Anesthetic Implications in a Child with Crouzon Syndrome
Crouzon syndrome (CS) is an autosomal dominant genetic disorder characterized by craniofacial dysostosis. Premature fusion of skull base leads to midfacial hypoplasia, shallow orbit, mandibular prognathism, overcrowding of upper teeth, high-arched palate, and upper airway obstruction. It is importan...
Autores principales: | , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Medknow Publications & Media Pvt Ltd
2017
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Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5341658/ https://www.ncbi.nlm.nih.gov/pubmed/28298794 http://dx.doi.org/10.4103/0259-1162.200234 |
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author | Kumar, Ajeet Goel, Nitika Sinha, Chandni Singh, Abhishek |
author_facet | Kumar, Ajeet Goel, Nitika Sinha, Chandni Singh, Abhishek |
author_sort | Kumar, Ajeet |
collection | PubMed |
description | Crouzon syndrome (CS) is an autosomal dominant genetic disorder characterized by craniofacial dysostosis. Premature fusion of skull base leads to midfacial hypoplasia, shallow orbit, mandibular prognathism, overcrowding of upper teeth, high-arched palate, and upper airway obstruction. It is important for anesthesiologists managing such patients to recognize and avoid potential airway complications. Here, we present a case of a 10-year-old child with CS posted for ptosis correction surgery. Use of peripheral nerve blocks to cut down opioid requirement, inhalational induction, and maintenance are key aspects in successful management of such cases. |
format | Online Article Text |
id | pubmed-5341658 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2017 |
publisher | Medknow Publications & Media Pvt Ltd |
record_format | MEDLINE/PubMed |
spelling | pubmed-53416582017-03-15 Anesthetic Implications in a Child with Crouzon Syndrome Kumar, Ajeet Goel, Nitika Sinha, Chandni Singh, Abhishek Anesth Essays Res Case Report Crouzon syndrome (CS) is an autosomal dominant genetic disorder characterized by craniofacial dysostosis. Premature fusion of skull base leads to midfacial hypoplasia, shallow orbit, mandibular prognathism, overcrowding of upper teeth, high-arched palate, and upper airway obstruction. It is important for anesthesiologists managing such patients to recognize and avoid potential airway complications. Here, we present a case of a 10-year-old child with CS posted for ptosis correction surgery. Use of peripheral nerve blocks to cut down opioid requirement, inhalational induction, and maintenance are key aspects in successful management of such cases. Medknow Publications & Media Pvt Ltd 2017 /pmc/articles/PMC5341658/ /pubmed/28298794 http://dx.doi.org/10.4103/0259-1162.200234 Text en Copyright: © 2017 Anesthesia: Essays and Researches http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open access article distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 3.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as the author is credited and the new creations are licensed under the identical terms. |
spellingShingle | Case Report Kumar, Ajeet Goel, Nitika Sinha, Chandni Singh, Abhishek Anesthetic Implications in a Child with Crouzon Syndrome |
title | Anesthetic Implications in a Child with Crouzon Syndrome |
title_full | Anesthetic Implications in a Child with Crouzon Syndrome |
title_fullStr | Anesthetic Implications in a Child with Crouzon Syndrome |
title_full_unstemmed | Anesthetic Implications in a Child with Crouzon Syndrome |
title_short | Anesthetic Implications in a Child with Crouzon Syndrome |
title_sort | anesthetic implications in a child with crouzon syndrome |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5341658/ https://www.ncbi.nlm.nih.gov/pubmed/28298794 http://dx.doi.org/10.4103/0259-1162.200234 |
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