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Myofibrillar Myopathies: New Perspectives from Animal Models to Potential Therapeutic Approaches

Myofibrillar myopathies (MFMs) are muscular disorders involving proteins that play a role in the structure, maintenance processes and protein quality control mechanisms closely related to the Z-disc in the muscular fibers. MFMs share common histological characteristics including progressive disorgan...

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Detalles Bibliográficos
Autores principales:	Batonnet-Pichon, Sabrina, Behin, Anthony, Cabet, Eva, Delort, Florence, Vicart, Patrick, Lilienbaum, Alain
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	IOS Press 2017
Materias:	Review
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5345645/ https://www.ncbi.nlm.nih.gov/pubmed/28269794 http://dx.doi.org/10.3233/JND-160203

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