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An unusual evolution of a case of Klippel-Trenaunay syndrome

Klippel–Trenaunay syndrome (KTS) is a rare congenital disorder. KTS can be diagnosed on the basis of any 2 of 3 features: cutaneous capillary malformations, soft tissue or bony hypertrophy and varicose veins. We present an unusual case of KTS complicated by an infection of venous ulcers of the lower...

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Autores principales: Martino, Valter, Ferrarese, Alessia, Alessandro, Borello, Bullano, Alberto, Marola, Silvia, Surace, Alessandra, Gentile, Valentina, Bindi, Marco, Solej, Mario, Enrico, Stefano
Formato: Online Artículo Texto
Lenguaje:English
Publicado: De Gruyter Open 2015
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5368873/
https://www.ncbi.nlm.nih.gov/pubmed/28352743
http://dx.doi.org/10.1515/med-2015-0084
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author Martino, Valter
Ferrarese, Alessia
Alessandro, Borello
Bullano, Alberto
Marola, Silvia
Surace, Alessandra
Gentile, Valentina
Bindi, Marco
Solej, Mario
Enrico, Stefano
author_facet Martino, Valter
Ferrarese, Alessia
Alessandro, Borello
Bullano, Alberto
Marola, Silvia
Surace, Alessandra
Gentile, Valentina
Bindi, Marco
Solej, Mario
Enrico, Stefano
author_sort Martino, Valter
collection PubMed
description Klippel–Trenaunay syndrome (KTS) is a rare congenital disorder. KTS can be diagnosed on the basis of any 2 of 3 features: cutaneous capillary malformations, soft tissue or bony hypertrophy and varicose veins. We present an unusual case of KTS complicated by an infection of venous ulcers of the lower limb by larvae. The treatment of infection was a complete debridement; however baseline treatment of KTS is still in evaluation.
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spelling pubmed-53688732017-03-28 An unusual evolution of a case of Klippel-Trenaunay syndrome Martino, Valter Ferrarese, Alessia Alessandro, Borello Bullano, Alberto Marola, Silvia Surace, Alessandra Gentile, Valentina Bindi, Marco Solej, Mario Enrico, Stefano Open Med (Wars) Research Article Klippel–Trenaunay syndrome (KTS) is a rare congenital disorder. KTS can be diagnosed on the basis of any 2 of 3 features: cutaneous capillary malformations, soft tissue or bony hypertrophy and varicose veins. We present an unusual case of KTS complicated by an infection of venous ulcers of the lower limb by larvae. The treatment of infection was a complete debridement; however baseline treatment of KTS is still in evaluation. De Gruyter Open 2015-12-17 /pmc/articles/PMC5368873/ /pubmed/28352743 http://dx.doi.org/10.1515/med-2015-0084 Text en © 2015 Valter Martino, et al. http://creativecommons.org/licenses/by-nc-nd/3.0 This work is licensed under the Creative Commons Attribution-NonCommercial-NoDerivs 3.0 License.
spellingShingle Research Article
Martino, Valter
Ferrarese, Alessia
Alessandro, Borello
Bullano, Alberto
Marola, Silvia
Surace, Alessandra
Gentile, Valentina
Bindi, Marco
Solej, Mario
Enrico, Stefano
An unusual evolution of a case of Klippel-Trenaunay syndrome
title An unusual evolution of a case of Klippel-Trenaunay syndrome
title_full An unusual evolution of a case of Klippel-Trenaunay syndrome
title_fullStr An unusual evolution of a case of Klippel-Trenaunay syndrome
title_full_unstemmed An unusual evolution of a case of Klippel-Trenaunay syndrome
title_short An unusual evolution of a case of Klippel-Trenaunay syndrome
title_sort unusual evolution of a case of klippel-trenaunay syndrome
topic Research Article
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5368873/
https://www.ncbi.nlm.nih.gov/pubmed/28352743
http://dx.doi.org/10.1515/med-2015-0084
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