Primary Synovial Sarcoma of the Orbit

PURPOSE: To describe the clinical, pathological, and immunohistochemical characteristics and therapies of a rare case of primary synovial sarcoma in the orbit. DESIGN: Retrospective interventional case report. PARTICIPANT: A 6-year-old girl with pathologically proven synovial sarcoma in the orbit. The diagnosis was confirmed by immunohistochemistry. METHODS: The patient was treated with right lateral orbital and right temporal tumor resection, followed by chemotherapy. She was followed up every 3 months for 1 year. RESULTS: The tumor was excised, and the patient received 5 courses of chemotherapy. She did well during the initial first-year follow-up with no recurrent signs. CONCLUSIONS: We reported the sixth case of primary synovial sarcoma in the orbit and the first case of a 6-year-old girl.