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Pheochromocytoma in a Child without Hypertension: A Contribution to the “Rule of 10s”

Pheochromocytoma (PCC) is a neuroendocrine tumor originating from chromaffin tissue in adrenal medulla. Its diagnosis and treatment are well defined in adults, but experience in children is limited. Children constitute only 10% of reported cases, the average age at presentation being 11 years. The m...

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Detalles Bibliográficos
Autores principales: Tripathy, Prasanta Kumar, Pattnaik, Kaumudee, Nayak, Manjushree, Mohanty, Hiranya Kishor
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2017
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5398108/
https://www.ncbi.nlm.nih.gov/pubmed/28469338
http://dx.doi.org/10.4103/0971-5851.203503
Descripción
Sumario:Pheochromocytoma (PCC) is a neuroendocrine tumor originating from chromaffin tissue in adrenal medulla. Its diagnosis and treatment are well defined in adults, but experience in children is limited. Children constitute only 10% of reported cases, the average age at presentation being 11 years. The most common presentation is sustained hypertension, which is absent in only 10% of children. We managed a 14-month-old female child with PCC, but she was not hypertensive. We report two unusual features, in this case, an extremely young age at presentation and a childhood case of nonhypertensive PCC contributing for “rule of 10s.”