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Ivemark syndrome: bronchial compression from anomalous pulmonary venous anatomy
Ivemark syndrome is a heterotaxy syndrome which affects multiple organs and affects roughly 1 in every 6000 deliveries. Specifically, it can cause total anomalous pulmonary venous return and cardiac defects, which ultimately lead to decreased life expectancy. In order to better understand the nature...
Autores principales: | , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Oxford University Press
2017
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5400418/ https://www.ncbi.nlm.nih.gov/pubmed/28458851 http://dx.doi.org/10.1093/jscr/rjx045 |
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author | Patel, Pooja H. Hayden, Joel Richardson, Randy |
author_facet | Patel, Pooja H. Hayden, Joel Richardson, Randy |
author_sort | Patel, Pooja H. |
collection | PubMed |
description | Ivemark syndrome is a heterotaxy syndrome which affects multiple organs and affects roughly 1 in every 6000 deliveries. Specifically, it can cause total anomalous pulmonary venous return and cardiac defects, which ultimately lead to decreased life expectancy. In order to better understand the nature of cardiac structures, CT angiogram has been heavily relied upon as it also allows for 3D reconstruction and optimal visualization of those features. This specific case presents with an anomalous venous return accompanied by multi-organ right isomerism that was reconstructed with 3D CT angiogram to better visualize and understand the cardiopulmonary system, as well as contribute to a fund of knowledge in hopes of discovering a solution to this condition. |
format | Online Article Text |
id | pubmed-5400418 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2017 |
publisher | Oxford University Press |
record_format | MEDLINE/PubMed |
spelling | pubmed-54004182017-04-28 Ivemark syndrome: bronchial compression from anomalous pulmonary venous anatomy Patel, Pooja H. Hayden, Joel Richardson, Randy J Surg Case Rep Case Report Ivemark syndrome is a heterotaxy syndrome which affects multiple organs and affects roughly 1 in every 6000 deliveries. Specifically, it can cause total anomalous pulmonary venous return and cardiac defects, which ultimately lead to decreased life expectancy. In order to better understand the nature of cardiac structures, CT angiogram has been heavily relied upon as it also allows for 3D reconstruction and optimal visualization of those features. This specific case presents with an anomalous venous return accompanied by multi-organ right isomerism that was reconstructed with 3D CT angiogram to better visualize and understand the cardiopulmonary system, as well as contribute to a fund of knowledge in hopes of discovering a solution to this condition. Oxford University Press 2017-03-17 /pmc/articles/PMC5400418/ /pubmed/28458851 http://dx.doi.org/10.1093/jscr/rjx045 Text en Published by Oxford University Press and JSCR Publishing Ltd. All rights reserved. © The Author 2017. http://creativecommons.org/licenses/by-nc/4.0/ This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/4.0/), which permits non-commercial re-use, distribution, and reproduction in any medium, provided the original work is properly cited. For commercial re-use, please contact journals.permissions@oup.com |
spellingShingle | Case Report Patel, Pooja H. Hayden, Joel Richardson, Randy Ivemark syndrome: bronchial compression from anomalous pulmonary venous anatomy |
title | Ivemark syndrome: bronchial compression from anomalous pulmonary venous anatomy |
title_full | Ivemark syndrome: bronchial compression from anomalous pulmonary venous anatomy |
title_fullStr | Ivemark syndrome: bronchial compression from anomalous pulmonary venous anatomy |
title_full_unstemmed | Ivemark syndrome: bronchial compression from anomalous pulmonary venous anatomy |
title_short | Ivemark syndrome: bronchial compression from anomalous pulmonary venous anatomy |
title_sort | ivemark syndrome: bronchial compression from anomalous pulmonary venous anatomy |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5400418/ https://www.ncbi.nlm.nih.gov/pubmed/28458851 http://dx.doi.org/10.1093/jscr/rjx045 |
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