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Ivemark syndrome: bronchial compression from anomalous pulmonary venous anatomy

Ivemark syndrome is a heterotaxy syndrome which affects multiple organs and affects roughly 1 in every 6000 deliveries. Specifically, it can cause total anomalous pulmonary venous return and cardiac defects, which ultimately lead to decreased life expectancy. In order to better understand the nature...

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Detalles Bibliográficos
Autores principales: Patel, Pooja H., Hayden, Joel, Richardson, Randy
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Oxford University Press 2017
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5400418/
https://www.ncbi.nlm.nih.gov/pubmed/28458851
http://dx.doi.org/10.1093/jscr/rjx045
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author Patel, Pooja H.
Hayden, Joel
Richardson, Randy
author_facet Patel, Pooja H.
Hayden, Joel
Richardson, Randy
author_sort Patel, Pooja H.
collection PubMed
description Ivemark syndrome is a heterotaxy syndrome which affects multiple organs and affects roughly 1 in every 6000 deliveries. Specifically, it can cause total anomalous pulmonary venous return and cardiac defects, which ultimately lead to decreased life expectancy. In order to better understand the nature of cardiac structures, CT angiogram has been heavily relied upon as it also allows for 3D reconstruction and optimal visualization of those features. This specific case presents with an anomalous venous return accompanied by multi-organ right isomerism that was reconstructed with 3D CT angiogram to better visualize and understand the cardiopulmonary system, as well as contribute to a fund of knowledge in hopes of discovering a solution to this condition.
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spelling pubmed-54004182017-04-28 Ivemark syndrome: bronchial compression from anomalous pulmonary venous anatomy Patel, Pooja H. Hayden, Joel Richardson, Randy J Surg Case Rep Case Report Ivemark syndrome is a heterotaxy syndrome which affects multiple organs and affects roughly 1 in every 6000 deliveries. Specifically, it can cause total anomalous pulmonary venous return and cardiac defects, which ultimately lead to decreased life expectancy. In order to better understand the nature of cardiac structures, CT angiogram has been heavily relied upon as it also allows for 3D reconstruction and optimal visualization of those features. This specific case presents with an anomalous venous return accompanied by multi-organ right isomerism that was reconstructed with 3D CT angiogram to better visualize and understand the cardiopulmonary system, as well as contribute to a fund of knowledge in hopes of discovering a solution to this condition. Oxford University Press 2017-03-17 /pmc/articles/PMC5400418/ /pubmed/28458851 http://dx.doi.org/10.1093/jscr/rjx045 Text en Published by Oxford University Press and JSCR Publishing Ltd. All rights reserved. © The Author 2017. http://creativecommons.org/licenses/by-nc/4.0/ This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/4.0/), which permits non-commercial re-use, distribution, and reproduction in any medium, provided the original work is properly cited. For commercial re-use, please contact journals.permissions@oup.com
spellingShingle Case Report
Patel, Pooja H.
Hayden, Joel
Richardson, Randy
Ivemark syndrome: bronchial compression from anomalous pulmonary venous anatomy
title Ivemark syndrome: bronchial compression from anomalous pulmonary venous anatomy
title_full Ivemark syndrome: bronchial compression from anomalous pulmonary venous anatomy
title_fullStr Ivemark syndrome: bronchial compression from anomalous pulmonary venous anatomy
title_full_unstemmed Ivemark syndrome: bronchial compression from anomalous pulmonary venous anatomy
title_short Ivemark syndrome: bronchial compression from anomalous pulmonary venous anatomy
title_sort ivemark syndrome: bronchial compression from anomalous pulmonary venous anatomy
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5400418/
https://www.ncbi.nlm.nih.gov/pubmed/28458851
http://dx.doi.org/10.1093/jscr/rjx045
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