Metastatic Intracranial Adenoid Cystic Carcinoma with Unknown Primary: Case Report and Review of Literature

Adenoid cystic carcinoma (ACC) is an epithelial malignancy comprising approximately 8–10% of all salivary gland tumors. Intracranial ACC without a known primary is an extremely rare pathobiological event. Only 13 cases have been reported in available literature. We report a case of a rare intracrani...

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Detalles Bibliográficos
Autores principales: Chaturvedi, Jitender, Konar, Subas Kanti, Jethwani, Dilip, Srinivas, Dwarakanath, Mahadevan, Anita
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2017
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5402499/
https://www.ncbi.nlm.nih.gov/pubmed/28479807
http://dx.doi.org/10.4103/0976-3147.203810
Descripción
Sumario:Adenoid cystic carcinoma (ACC) is an epithelial malignancy comprising approximately 8–10% of all salivary gland tumors. Intracranial ACC without a known primary is an extremely rare pathobiological event. Only 13 cases have been reported in available literature. We report a case of a rare intracranial ACC in a 35-year-old gentleman presenting with features of raised intracranial pressure. Patient had a lesion in the right parieto-occipital lobe and underwent gross total decompression. There was no evidence of any primary after a thorough systemic evaluation. In the postoperative period, he showed a good clinical improvement and was recurrence free at follow-up of 18 months. We also discuss and review the existing relevant literature.

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