Cargando…
Herlyn-Werner-Wunderlich Syndrome: Sonographic and Magnetic Resonance (MR) Imaging Findings of This Rare Urogenital Anomaly
BACKGROUND: Herlyn-Werner-Wunderlich syndrome is a rare congenital urogenital anomaly characterised by uterus didelphys with blind hemivagina and ipsilateral renal agenesis. Children usually have progressive pelvic pain after menarche, palpable mass due to hemihaemato(metro)colpos or pelvic inflamma...
Autores principales: | , , |
---|---|
Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
International Scientific Literature, Inc.
2017
|
Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5402867/ https://www.ncbi.nlm.nih.gov/pubmed/28469738 http://dx.doi.org/10.12659/PJR.899889 |
_version_ | 1783231313977802752 |
---|---|
author | Yilmaz, Sukriye Yildiz, Adalet Elcin Fitoz, Suat |
author_facet | Yilmaz, Sukriye Yildiz, Adalet Elcin Fitoz, Suat |
author_sort | Yilmaz, Sukriye |
collection | PubMed |
description | BACKGROUND: Herlyn-Werner-Wunderlich syndrome is a rare congenital urogenital anomaly characterised by uterus didelphys with blind hemivagina and ipsilateral renal agenesis. Children usually have progressive pelvic pain after menarche, palpable mass due to hemihaemato(metro)colpos or pelvic inflammatory disease. The diagnosis usually requires a suspicion of this rare genitourinary syndrome. CASE REPORTS: We present ultrasonography and MR imaging findings of this rare anomaly in two cases. CONCLUSIONS: Early recognition of this rare syndrome can lead to an immediate, proper surgical intervention and is necessary to prevent complications and preserve future fertility. Ultrasound and MR imaging findings can collectively delineate uterine morphology, indicate the absence of ipsilateral kidney and show obstructed hemivagina. |
format | Online Article Text |
id | pubmed-5402867 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2017 |
publisher | International Scientific Literature, Inc. |
record_format | MEDLINE/PubMed |
spelling | pubmed-54028672017-05-03 Herlyn-Werner-Wunderlich Syndrome: Sonographic and Magnetic Resonance (MR) Imaging Findings of This Rare Urogenital Anomaly Yilmaz, Sukriye Yildiz, Adalet Elcin Fitoz, Suat Pol J Radiol Case Report BACKGROUND: Herlyn-Werner-Wunderlich syndrome is a rare congenital urogenital anomaly characterised by uterus didelphys with blind hemivagina and ipsilateral renal agenesis. Children usually have progressive pelvic pain after menarche, palpable mass due to hemihaemato(metro)colpos or pelvic inflammatory disease. The diagnosis usually requires a suspicion of this rare genitourinary syndrome. CASE REPORTS: We present ultrasonography and MR imaging findings of this rare anomaly in two cases. CONCLUSIONS: Early recognition of this rare syndrome can lead to an immediate, proper surgical intervention and is necessary to prevent complications and preserve future fertility. Ultrasound and MR imaging findings can collectively delineate uterine morphology, indicate the absence of ipsilateral kidney and show obstructed hemivagina. International Scientific Literature, Inc. 2017-04-16 /pmc/articles/PMC5402867/ /pubmed/28469738 http://dx.doi.org/10.12659/PJR.899889 Text en © Pol J Radiol, 2017 This is an open access article. Unrestricted non-commercial use is permitted provided the original work is properly cited. |
spellingShingle | Case Report Yilmaz, Sukriye Yildiz, Adalet Elcin Fitoz, Suat Herlyn-Werner-Wunderlich Syndrome: Sonographic and Magnetic Resonance (MR) Imaging Findings of This Rare Urogenital Anomaly |
title | Herlyn-Werner-Wunderlich Syndrome: Sonographic and Magnetic Resonance (MR) Imaging Findings of This Rare Urogenital Anomaly |
title_full | Herlyn-Werner-Wunderlich Syndrome: Sonographic and Magnetic Resonance (MR) Imaging Findings of This Rare Urogenital Anomaly |
title_fullStr | Herlyn-Werner-Wunderlich Syndrome: Sonographic and Magnetic Resonance (MR) Imaging Findings of This Rare Urogenital Anomaly |
title_full_unstemmed | Herlyn-Werner-Wunderlich Syndrome: Sonographic and Magnetic Resonance (MR) Imaging Findings of This Rare Urogenital Anomaly |
title_short | Herlyn-Werner-Wunderlich Syndrome: Sonographic and Magnetic Resonance (MR) Imaging Findings of This Rare Urogenital Anomaly |
title_sort | herlyn-werner-wunderlich syndrome: sonographic and magnetic resonance (mr) imaging findings of this rare urogenital anomaly |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5402867/ https://www.ncbi.nlm.nih.gov/pubmed/28469738 http://dx.doi.org/10.12659/PJR.899889 |
work_keys_str_mv | AT yilmazsukriye herlynwernerwunderlichsyndromesonographicandmagneticresonancemrimagingfindingsofthisrareurogenitalanomaly AT yildizadaletelcin herlynwernerwunderlichsyndromesonographicandmagneticresonancemrimagingfindingsofthisrareurogenitalanomaly AT fitozsuat herlynwernerwunderlichsyndromesonographicandmagneticresonancemrimagingfindingsofthisrareurogenitalanomaly |