Syndrome d’activation macrophagique compliquant une lymphohistiocytose familiale

Macrophage activation syndrome (MAS) is an anatomoclinic entity due to inappropriate macrophage activation. It is a rare pathology, characterized by clinical signs that are not very specific and by biological elements. Their association must evoke the diagnosis. It can be classified as primary or se...

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Autores principales: Boussaadni, Yousra El, Benajiba, Noufissa, Bousfiha, Ahmed Aziz, Ailal, Fatima
Formato: Online Artículo Texto
Lenguaje:English
Publicado: The African Field Epidemiology Network 2017
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5410000/
https://www.ncbi.nlm.nih.gov/pubmed/28491224
http://dx.doi.org/10.11604/pamj.2017.26.93.6235
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author Boussaadni, Yousra El
Benajiba, Noufissa
Bousfiha, Ahmed Aziz
Ailal, Fatima
author_facet Boussaadni, Yousra El
Benajiba, Noufissa
Bousfiha, Ahmed Aziz
Ailal, Fatima
author_sort Boussaadni, Yousra El
collection PubMed
description Macrophage activation syndrome (MAS) is an anatomoclinic entity due to inappropriate macrophage activation. It is a rare pathology, characterized by clinical signs that are not very specific and by biological elements. Their association must evoke the diagnosis. It can be classified as primary or secondary, its prognosis is still unclear. We report the case of a 3-year and 4-month-old infant admitted to our department with primary MAS in order to remind clinicians the importance of suspecting primary cause in specific situations.
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spelling pubmed-54100002017-05-10 Syndrome d’activation macrophagique compliquant une lymphohistiocytose familiale Boussaadni, Yousra El Benajiba, Noufissa Bousfiha, Ahmed Aziz Ailal, Fatima Pan Afr Med J Case Report Macrophage activation syndrome (MAS) is an anatomoclinic entity due to inappropriate macrophage activation. It is a rare pathology, characterized by clinical signs that are not very specific and by biological elements. Their association must evoke the diagnosis. It can be classified as primary or secondary, its prognosis is still unclear. We report the case of a 3-year and 4-month-old infant admitted to our department with primary MAS in order to remind clinicians the importance of suspecting primary cause in specific situations. The African Field Epidemiology Network 2017-02-24 /pmc/articles/PMC5410000/ /pubmed/28491224 http://dx.doi.org/10.11604/pamj.2017.26.93.6235 Text en © Yousra El Boussaadni et al. http://creativecommons.org/licenses/by/2.0/ The Pan African Medical Journal - ISSN 1937-8688. This is an Open Access article distributed under the terms of the Creative Commons Attribution License which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Boussaadni, Yousra El
Benajiba, Noufissa
Bousfiha, Ahmed Aziz
Ailal, Fatima
Syndrome d’activation macrophagique compliquant une lymphohistiocytose familiale
title Syndrome d’activation macrophagique compliquant une lymphohistiocytose familiale
title_full Syndrome d’activation macrophagique compliquant une lymphohistiocytose familiale
title_fullStr Syndrome d’activation macrophagique compliquant une lymphohistiocytose familiale
title_full_unstemmed Syndrome d’activation macrophagique compliquant une lymphohistiocytose familiale
title_short Syndrome d’activation macrophagique compliquant une lymphohistiocytose familiale
title_sort syndrome d’activation macrophagique compliquant une lymphohistiocytose familiale
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5410000/
https://www.ncbi.nlm.nih.gov/pubmed/28491224
http://dx.doi.org/10.11604/pamj.2017.26.93.6235
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AT bousfihaahmedaziz syndromedactivationmacrophagiquecompliquantunelymphohistiocytosefamiliale
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