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An Unusual Presentation of Congenital Lobar Emphysema

Congenital lobar emphysema is an uncommon bronchopulmonary malformation characterized by lobar overinflation and accompanying alveolar septum damage that leads to compression atelectasis of the lung parenchyma and displacement of mediastinal structures, with the resultant ventilation-perfusion misma...

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Detalles Bibliográficos
Autores principales: Arnaud, Daniel, Varon, Joseph, Surani, Salim
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Hindawi 2017
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5421086/
https://www.ncbi.nlm.nih.gov/pubmed/28523200
http://dx.doi.org/10.1155/2017/6719617
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author Arnaud, Daniel
Varon, Joseph
Surani, Salim
author_facet Arnaud, Daniel
Varon, Joseph
Surani, Salim
author_sort Arnaud, Daniel
collection PubMed
description Congenital lobar emphysema is an uncommon bronchopulmonary malformation characterized by lobar overinflation and accompanying alveolar septum damage that leads to compression atelectasis of the lung parenchyma and displacement of mediastinal structures, with the resultant ventilation-perfusion mismatch. We present a case of a 33-year-old lady with progressive exertional dyspnea. Chest radiograph findings lead to the suspicion of congenital lobar emphysema, which was then confirmed by a computed tomography (CT) scan. This condition is most commonly identified in newborns, with very few cases being reported in adults. Lobectomy remains the treatment of choice and in general has good outcome.
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spelling pubmed-54210862017-05-18 An Unusual Presentation of Congenital Lobar Emphysema Arnaud, Daniel Varon, Joseph Surani, Salim Case Rep Pulmonol Case Report Congenital lobar emphysema is an uncommon bronchopulmonary malformation characterized by lobar overinflation and accompanying alveolar septum damage that leads to compression atelectasis of the lung parenchyma and displacement of mediastinal structures, with the resultant ventilation-perfusion mismatch. We present a case of a 33-year-old lady with progressive exertional dyspnea. Chest radiograph findings lead to the suspicion of congenital lobar emphysema, which was then confirmed by a computed tomography (CT) scan. This condition is most commonly identified in newborns, with very few cases being reported in adults. Lobectomy remains the treatment of choice and in general has good outcome. Hindawi 2017 2017-04-24 /pmc/articles/PMC5421086/ /pubmed/28523200 http://dx.doi.org/10.1155/2017/6719617 Text en Copyright © 2017 Daniel Arnaud et al. https://creativecommons.org/licenses/by/4.0/ This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Arnaud, Daniel
Varon, Joseph
Surani, Salim
An Unusual Presentation of Congenital Lobar Emphysema
title An Unusual Presentation of Congenital Lobar Emphysema
title_full An Unusual Presentation of Congenital Lobar Emphysema
title_fullStr An Unusual Presentation of Congenital Lobar Emphysema
title_full_unstemmed An Unusual Presentation of Congenital Lobar Emphysema
title_short An Unusual Presentation of Congenital Lobar Emphysema
title_sort unusual presentation of congenital lobar emphysema
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5421086/
https://www.ncbi.nlm.nih.gov/pubmed/28523200
http://dx.doi.org/10.1155/2017/6719617
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