Cargando…
An Unusual Presentation of Congenital Lobar Emphysema
Congenital lobar emphysema is an uncommon bronchopulmonary malformation characterized by lobar overinflation and accompanying alveolar septum damage that leads to compression atelectasis of the lung parenchyma and displacement of mediastinal structures, with the resultant ventilation-perfusion misma...
Autores principales: | , , |
---|---|
Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Hindawi
2017
|
Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5421086/ https://www.ncbi.nlm.nih.gov/pubmed/28523200 http://dx.doi.org/10.1155/2017/6719617 |
_version_ | 1783234532750655488 |
---|---|
author | Arnaud, Daniel Varon, Joseph Surani, Salim |
author_facet | Arnaud, Daniel Varon, Joseph Surani, Salim |
author_sort | Arnaud, Daniel |
collection | PubMed |
description | Congenital lobar emphysema is an uncommon bronchopulmonary malformation characterized by lobar overinflation and accompanying alveolar septum damage that leads to compression atelectasis of the lung parenchyma and displacement of mediastinal structures, with the resultant ventilation-perfusion mismatch. We present a case of a 33-year-old lady with progressive exertional dyspnea. Chest radiograph findings lead to the suspicion of congenital lobar emphysema, which was then confirmed by a computed tomography (CT) scan. This condition is most commonly identified in newborns, with very few cases being reported in adults. Lobectomy remains the treatment of choice and in general has good outcome. |
format | Online Article Text |
id | pubmed-5421086 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2017 |
publisher | Hindawi |
record_format | MEDLINE/PubMed |
spelling | pubmed-54210862017-05-18 An Unusual Presentation of Congenital Lobar Emphysema Arnaud, Daniel Varon, Joseph Surani, Salim Case Rep Pulmonol Case Report Congenital lobar emphysema is an uncommon bronchopulmonary malformation characterized by lobar overinflation and accompanying alveolar septum damage that leads to compression atelectasis of the lung parenchyma and displacement of mediastinal structures, with the resultant ventilation-perfusion mismatch. We present a case of a 33-year-old lady with progressive exertional dyspnea. Chest radiograph findings lead to the suspicion of congenital lobar emphysema, which was then confirmed by a computed tomography (CT) scan. This condition is most commonly identified in newborns, with very few cases being reported in adults. Lobectomy remains the treatment of choice and in general has good outcome. Hindawi 2017 2017-04-24 /pmc/articles/PMC5421086/ /pubmed/28523200 http://dx.doi.org/10.1155/2017/6719617 Text en Copyright © 2017 Daniel Arnaud et al. https://creativecommons.org/licenses/by/4.0/ This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited. |
spellingShingle | Case Report Arnaud, Daniel Varon, Joseph Surani, Salim An Unusual Presentation of Congenital Lobar Emphysema |
title | An Unusual Presentation of Congenital Lobar Emphysema |
title_full | An Unusual Presentation of Congenital Lobar Emphysema |
title_fullStr | An Unusual Presentation of Congenital Lobar Emphysema |
title_full_unstemmed | An Unusual Presentation of Congenital Lobar Emphysema |
title_short | An Unusual Presentation of Congenital Lobar Emphysema |
title_sort | unusual presentation of congenital lobar emphysema |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5421086/ https://www.ncbi.nlm.nih.gov/pubmed/28523200 http://dx.doi.org/10.1155/2017/6719617 |
work_keys_str_mv | AT arnauddaniel anunusualpresentationofcongenitallobaremphysema AT varonjoseph anunusualpresentationofcongenitallobaremphysema AT suranisalim anunusualpresentationofcongenitallobaremphysema AT arnauddaniel unusualpresentationofcongenitallobaremphysema AT varonjoseph unusualpresentationofcongenitallobaremphysema AT suranisalim unusualpresentationofcongenitallobaremphysema |