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Clinicopathological features and outcome of chronic lymphocytic leukaemia in Chinese patients

Chronic lymphocytic leukaemia (CLL) is uncommon in Chinese population and its biology, genetics and treatment outcome in Chinese patients have not been comprehensively investigated. In this study, we studied the clinicopathological features and outcome of 212 Chinese patients with newly diagnosed CL...

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Autores principales: Chan, Thomas Sau-Yan, Lee, Yuh-Shan, Giudice, Ilaria Del, Marinelli, Marilisa, Ilari, Caterina, Cafforio, Luciana, Guarini, Anna, Tan, Daryl, Phipps, Colin, Goh, Yeow-Tee, Hwang, William, Goh, Allan Zhi-Kai, Siu, Lisa Lai-Ping, Wu, Saliangi, Ha, Chun-Yin, Lin, Shek-Ying, Kwok, Chi-Hang, Lau, Chi-Kuen, Wong, Kit-Fai, Foà, Robin, Kwong, Yok-Lam, Tse, Eric
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Impact Journals LLC 2017
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5421943/
https://www.ncbi.nlm.nih.gov/pubmed/28424415
http://dx.doi.org/10.18632/oncotarget.16037
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author Chan, Thomas Sau-Yan
Lee, Yuh-Shan
Giudice, Ilaria Del
Marinelli, Marilisa
Ilari, Caterina
Cafforio, Luciana
Guarini, Anna
Tan, Daryl
Phipps, Colin
Goh, Yeow-Tee
Hwang, William
Goh, Allan Zhi-Kai
Siu, Lisa Lai-Ping
Wu, Saliangi
Ha, Chun-Yin
Lin, Shek-Ying
Kwok, Chi-Hang
Lau, Chi-Kuen
Wong, Kit-Fai
Foà, Robin
Kwong, Yok-Lam
Tse, Eric
author_facet Chan, Thomas Sau-Yan
Lee, Yuh-Shan
Giudice, Ilaria Del
Marinelli, Marilisa
Ilari, Caterina
Cafforio, Luciana
Guarini, Anna
Tan, Daryl
Phipps, Colin
Goh, Yeow-Tee
Hwang, William
Goh, Allan Zhi-Kai
Siu, Lisa Lai-Ping
Wu, Saliangi
Ha, Chun-Yin
Lin, Shek-Ying
Kwok, Chi-Hang
Lau, Chi-Kuen
Wong, Kit-Fai
Foà, Robin
Kwong, Yok-Lam
Tse, Eric
author_sort Chan, Thomas Sau-Yan
collection PubMed
description Chronic lymphocytic leukaemia (CLL) is uncommon in Chinese population and its biology, genetics and treatment outcome in Chinese patients have not been comprehensively investigated. In this study, we studied the clinicopathological features and outcome of 212 Chinese patients with newly diagnosed CLL in Hong Kong and Singapore. The median age at diagnosis was 64 years. The majority of patients presented with early-stage disease (Binet stage A, 56.1%). Del(13)(q14) was the most frequent abnormality (41.7%) detected by fluorescence in situ hybridization (FISH) analysis. Del(17p) and TP53 gene mutations were detected in 7.8% and 8.2% of patients, respectively. MYD88 mutations were found at a higher frequency (11.5%) than expected. CLL with unmutated variable region of the immunoglobulin heavy chain genes (IGHV) occurred in only 31.2% of cases, and was associated with advanced-stage disease (p <0.01) and adverse FISH abnormalities (p<0.01). With a median follow-up of 39 months, the median overall survival (OS) was 108 months. The presence of del(17p) or TP53 mutations was associated with a significantly shorter time to first treatment and an inferior OS (p <0.01). Unmutated IGHV was also associated with a significantly shorter time to treatment (p <0.01). Among patients who required treatment, the median OS and progression-free survival (PFS) were 107 and 23 months, respectively. The presence of del(17p) was associated with a significantly inferior OS and PFS (p <0.01). In summary, Chinese CLL patients had similar genetic aberrations at diagnosis compared with those of Western populations. FISH abnormalities are major factors affecting outcome.
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spelling pubmed-54219432017-05-10 Clinicopathological features and outcome of chronic lymphocytic leukaemia in Chinese patients Chan, Thomas Sau-Yan Lee, Yuh-Shan Giudice, Ilaria Del Marinelli, Marilisa Ilari, Caterina Cafforio, Luciana Guarini, Anna Tan, Daryl Phipps, Colin Goh, Yeow-Tee Hwang, William Goh, Allan Zhi-Kai Siu, Lisa Lai-Ping Wu, Saliangi Ha, Chun-Yin Lin, Shek-Ying Kwok, Chi-Hang Lau, Chi-Kuen Wong, Kit-Fai Foà, Robin Kwong, Yok-Lam Tse, Eric Oncotarget Research Paper Chronic lymphocytic leukaemia (CLL) is uncommon in Chinese population and its biology, genetics and treatment outcome in Chinese patients have not been comprehensively investigated. In this study, we studied the clinicopathological features and outcome of 212 Chinese patients with newly diagnosed CLL in Hong Kong and Singapore. The median age at diagnosis was 64 years. The majority of patients presented with early-stage disease (Binet stage A, 56.1%). Del(13)(q14) was the most frequent abnormality (41.7%) detected by fluorescence in situ hybridization (FISH) analysis. Del(17p) and TP53 gene mutations were detected in 7.8% and 8.2% of patients, respectively. MYD88 mutations were found at a higher frequency (11.5%) than expected. CLL with unmutated variable region of the immunoglobulin heavy chain genes (IGHV) occurred in only 31.2% of cases, and was associated with advanced-stage disease (p <0.01) and adverse FISH abnormalities (p<0.01). With a median follow-up of 39 months, the median overall survival (OS) was 108 months. The presence of del(17p) or TP53 mutations was associated with a significantly shorter time to first treatment and an inferior OS (p <0.01). Unmutated IGHV was also associated with a significantly shorter time to treatment (p <0.01). Among patients who required treatment, the median OS and progression-free survival (PFS) were 107 and 23 months, respectively. The presence of del(17p) was associated with a significantly inferior OS and PFS (p <0.01). In summary, Chinese CLL patients had similar genetic aberrations at diagnosis compared with those of Western populations. FISH abnormalities are major factors affecting outcome. Impact Journals LLC 2017-03-09 /pmc/articles/PMC5421943/ /pubmed/28424415 http://dx.doi.org/10.18632/oncotarget.16037 Text en Copyright: © 2017 Chan et al. http://creativecommons.org/licenses/by/3.0/ This is an open-access article distributed under the terms of the Creative Commons Attribution License (http://creativecommons.org/licenses/by/3.0/) (CC-BY), which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.
spellingShingle Research Paper
Chan, Thomas Sau-Yan
Lee, Yuh-Shan
Giudice, Ilaria Del
Marinelli, Marilisa
Ilari, Caterina
Cafforio, Luciana
Guarini, Anna
Tan, Daryl
Phipps, Colin
Goh, Yeow-Tee
Hwang, William
Goh, Allan Zhi-Kai
Siu, Lisa Lai-Ping
Wu, Saliangi
Ha, Chun-Yin
Lin, Shek-Ying
Kwok, Chi-Hang
Lau, Chi-Kuen
Wong, Kit-Fai
Foà, Robin
Kwong, Yok-Lam
Tse, Eric
Clinicopathological features and outcome of chronic lymphocytic leukaemia in Chinese patients
title Clinicopathological features and outcome of chronic lymphocytic leukaemia in Chinese patients
title_full Clinicopathological features and outcome of chronic lymphocytic leukaemia in Chinese patients
title_fullStr Clinicopathological features and outcome of chronic lymphocytic leukaemia in Chinese patients
title_full_unstemmed Clinicopathological features and outcome of chronic lymphocytic leukaemia in Chinese patients
title_short Clinicopathological features and outcome of chronic lymphocytic leukaemia in Chinese patients
title_sort clinicopathological features and outcome of chronic lymphocytic leukaemia in chinese patients
topic Research Paper
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5421943/
https://www.ncbi.nlm.nih.gov/pubmed/28424415
http://dx.doi.org/10.18632/oncotarget.16037
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