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Multidisciplinary surgical treatment of presacral meningocele and teratoma in an adult with Currarino triad
BACKGROUND: Currarino syndrome (CS) is a rare genetic condition that presents with the defining triad of anorectal malformations, sacral bone deformations, and presacral masses, which may include teratoma. Neurosurgeons are involved in the surgical treatment of anterior meningoceles, which are often...
Autores principales: | , , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Medknow Publications & Media Pvt Ltd
2017
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5445655/ https://www.ncbi.nlm.nih.gov/pubmed/28584680 http://dx.doi.org/10.4103/sni.sni_439_16 |
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author | Chakhalian, Daniel Gunasekaran, Arunprasad Gandhi, Gautam Bradley, Lucas Mizell, Jason Kazemi, Noojan |
author_facet | Chakhalian, Daniel Gunasekaran, Arunprasad Gandhi, Gautam Bradley, Lucas Mizell, Jason Kazemi, Noojan |
author_sort | Chakhalian, Daniel |
collection | PubMed |
description | BACKGROUND: Currarino syndrome (CS) is a rare genetic condition that presents with the defining triad of anorectal malformations, sacral bone deformations, and presacral masses, which may include teratoma. Neurosurgeons are involved in the surgical treatment of anterior meningoceles, which are often associated with this condition. The accepted surgical treatment is a staged anterior-posterior resection of the presacral mass and obliteration of the anterior meningocele. CASE DESCRIPTION: This case involved a 36-year-old female who presented with late onset of symptoms attributed to CS (e.g., presacral mass, anterior sacral meningocele, and sacral agenesis). She successfully underwent multidisciplinary single-stage approach for treatment of the anterior sacral meningocele and resection of the presacral mass. This required obliteration of the meningocele and closure of the dural defect. One year later, her meningocele had fully resolved. CONCLUSION: While late presentations with CS are rare, early detection and multidisciplinary treatment including single-state anterior may be successful for managing these patients. |
format | Online Article Text |
id | pubmed-5445655 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2017 |
publisher | Medknow Publications & Media Pvt Ltd |
record_format | MEDLINE/PubMed |
spelling | pubmed-54456552017-06-05 Multidisciplinary surgical treatment of presacral meningocele and teratoma in an adult with Currarino triad Chakhalian, Daniel Gunasekaran, Arunprasad Gandhi, Gautam Bradley, Lucas Mizell, Jason Kazemi, Noojan Surg Neurol Int Unique Case Observations: Case Report BACKGROUND: Currarino syndrome (CS) is a rare genetic condition that presents with the defining triad of anorectal malformations, sacral bone deformations, and presacral masses, which may include teratoma. Neurosurgeons are involved in the surgical treatment of anterior meningoceles, which are often associated with this condition. The accepted surgical treatment is a staged anterior-posterior resection of the presacral mass and obliteration of the anterior meningocele. CASE DESCRIPTION: This case involved a 36-year-old female who presented with late onset of symptoms attributed to CS (e.g., presacral mass, anterior sacral meningocele, and sacral agenesis). She successfully underwent multidisciplinary single-stage approach for treatment of the anterior sacral meningocele and resection of the presacral mass. This required obliteration of the meningocele and closure of the dural defect. One year later, her meningocele had fully resolved. CONCLUSION: While late presentations with CS are rare, early detection and multidisciplinary treatment including single-state anterior may be successful for managing these patients. Medknow Publications & Media Pvt Ltd 2017-05-10 /pmc/articles/PMC5445655/ /pubmed/28584680 http://dx.doi.org/10.4103/sni.sni_439_16 Text en Copyright: © 2017 Surgical Neurology International http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open access article distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 3.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as the author is credited and the new creations are licensed under the identical terms. |
spellingShingle | Unique Case Observations: Case Report Chakhalian, Daniel Gunasekaran, Arunprasad Gandhi, Gautam Bradley, Lucas Mizell, Jason Kazemi, Noojan Multidisciplinary surgical treatment of presacral meningocele and teratoma in an adult with Currarino triad |
title | Multidisciplinary surgical treatment of presacral meningocele and teratoma in an adult with Currarino triad |
title_full | Multidisciplinary surgical treatment of presacral meningocele and teratoma in an adult with Currarino triad |
title_fullStr | Multidisciplinary surgical treatment of presacral meningocele and teratoma in an adult with Currarino triad |
title_full_unstemmed | Multidisciplinary surgical treatment of presacral meningocele and teratoma in an adult with Currarino triad |
title_short | Multidisciplinary surgical treatment of presacral meningocele and teratoma in an adult with Currarino triad |
title_sort | multidisciplinary surgical treatment of presacral meningocele and teratoma in an adult with currarino triad |
topic | Unique Case Observations: Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5445655/ https://www.ncbi.nlm.nih.gov/pubmed/28584680 http://dx.doi.org/10.4103/sni.sni_439_16 |
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