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A Patient with MSUD: Acute Management with Sodium Phenylacetate/Sodium Benzoate and Sodium Phenylbutyrate

In treatment of metabolic imbalances caused by maple syrup urine disease (MSUD), peritoneal dialysis, and hemofiltration, pharmacological treatments for elimination of toxic metabolites can be used in addition to basic dietary modifications. Therapy with sodium phenylacetate/benzoate or sodium pheny...

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Detalles Bibliográficos
Autores principales:	Köse, Melis, Canda, Ebru, Kagnici, Mehtap, Uçar, Sema Kalkan, Çoker, Mahmut
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Hindawi 2017
Materias:	Case Report
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5447276/ https://www.ncbi.nlm.nih.gov/pubmed/28589054 http://dx.doi.org/10.1155/2017/1045031

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