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Dicephalus dipus dibrachius twins: report of an autopsy case

Dicephalus dipus dibrachius twins are a rare form of conjoined twins. An autopsy of conjoined dicephalus twins is reported. The diagnosis was performed during the pregnancy and the family received a judicial authorization for termination of pregnancy. The preterm newborn progressed to cardiac arrest...

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Autores principales: Oliveira, Cristiano Claudino, Rainho, Claudia Aparecida, Domingues, Maria Aparecida Custódio
Formato: Online Artículo Texto
Lenguaje:English
Publicado: São Paulo, SP: Universidade de São Paulo, Hospital Universitário 2014
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5448298/
https://www.ncbi.nlm.nih.gov/pubmed/28580323
http://dx.doi.org/10.4322/acr.2014.018
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author Oliveira, Cristiano Claudino
Rainho, Claudia Aparecida
Domingues, Maria Aparecida Custódio
author_facet Oliveira, Cristiano Claudino
Rainho, Claudia Aparecida
Domingues, Maria Aparecida Custódio
author_sort Oliveira, Cristiano Claudino
collection PubMed
description Dicephalus dipus dibrachius twins are a rare form of conjoined twins. An autopsy of conjoined dicephalus twins is reported. The diagnosis was performed during the pregnancy and the family received a judicial authorization for termination of pregnancy. The preterm newborn progressed to cardiac arrest and died following a court order to terminate the pregnancy. The conceptus presented two arms, two legs, a trunk, two heads, and a single umbilical cord. The two spinal columns presented vertebral fusion in the sacral region. The heart exhibited complex malformations. The external genitalia were female; and cytogenetic analysis confirmed female sex (46, XX). This analysis also corroborated the etiopathogenic hypotheses described for this abnormality, which proposes failures in embryonic formation rather than specific chromosomal alterations. Current identification of cases by ultrasound permits medical management and multidisciplinary action with the family, enabling the legal termination of pregnancy.
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spelling pubmed-54482982017-06-02 Dicephalus dipus dibrachius twins: report of an autopsy case Oliveira, Cristiano Claudino Rainho, Claudia Aparecida Domingues, Maria Aparecida Custódio Autops Case Rep Article / Autopsy Case Report Dicephalus dipus dibrachius twins are a rare form of conjoined twins. An autopsy of conjoined dicephalus twins is reported. The diagnosis was performed during the pregnancy and the family received a judicial authorization for termination of pregnancy. The preterm newborn progressed to cardiac arrest and died following a court order to terminate the pregnancy. The conceptus presented two arms, two legs, a trunk, two heads, and a single umbilical cord. The two spinal columns presented vertebral fusion in the sacral region. The heart exhibited complex malformations. The external genitalia were female; and cytogenetic analysis confirmed female sex (46, XX). This analysis also corroborated the etiopathogenic hypotheses described for this abnormality, which proposes failures in embryonic formation rather than specific chromosomal alterations. Current identification of cases by ultrasound permits medical management and multidisciplinary action with the family, enabling the legal termination of pregnancy. São Paulo, SP: Universidade de São Paulo, Hospital Universitário 2014-06-30 /pmc/articles/PMC5448298/ /pubmed/28580323 http://dx.doi.org/10.4322/acr.2014.018 Text en Autopsy and Case Reports. ISSN 2236-1960. Copyright © 2014. http://creativecommons.org/licenses/by-nc/3.0/ This is an Open Access article distributed of terms of the Creative Commons Attribution Non-Commercial License which permits unrestricted non-commercial use, distribution, and reproduction in any medium provided article is properly cited.
spellingShingle Article / Autopsy Case Report
Oliveira, Cristiano Claudino
Rainho, Claudia Aparecida
Domingues, Maria Aparecida Custódio
Dicephalus dipus dibrachius twins: report of an autopsy case
title Dicephalus dipus dibrachius twins: report of an autopsy case
title_full Dicephalus dipus dibrachius twins: report of an autopsy case
title_fullStr Dicephalus dipus dibrachius twins: report of an autopsy case
title_full_unstemmed Dicephalus dipus dibrachius twins: report of an autopsy case
title_short Dicephalus dipus dibrachius twins: report of an autopsy case
title_sort dicephalus dipus dibrachius twins: report of an autopsy case
topic Article / Autopsy Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5448298/
https://www.ncbi.nlm.nih.gov/pubmed/28580323
http://dx.doi.org/10.4322/acr.2014.018
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