A Challenging Case of Hepatoblastoma Concomitant with Autosomal Recessive Polycystic Kidney Disease and Caroli Syndrome—Review of the Literature

We report a rare case of an 18-month-old female with autosomal recessive polycystic kidney disease, Caroli syndrome, and pure fetal type hepatoblastoma. The liver tumor was surgically resected with no chemotherapy given. Now 9 years post resection she demonstrates no local or distant recurrence and...

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Detalles Bibliográficos
Autores principales: Kadakia, Nevil, Lobritto, Steven J., Ovchinsky, Nadia, Remotti, Helen E., Yamashiro, Darrell J., Emond, Jean C., Martinez, Mercedes
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Frontiers Media S.A. 2017
Materias:
Pediatrics
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5461266/
https://www.ncbi.nlm.nih.gov/pubmed/28638817
http://dx.doi.org/10.3389/fped.2017.00114
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author Kadakia, Nevil
Lobritto, Steven J.
Ovchinsky, Nadia
Remotti, Helen E.
Yamashiro, Darrell J.
Emond, Jean C.
Martinez, Mercedes
author_facet Kadakia, Nevil
Lobritto, Steven J.
Ovchinsky, Nadia
Remotti, Helen E.
Yamashiro, Darrell J.
Emond, Jean C.
Martinez, Mercedes
author_sort Kadakia, Nevil
collection PubMed
description We report a rare case of an 18-month-old female with autosomal recessive polycystic kidney disease, Caroli syndrome, and pure fetal type hepatoblastoma. The liver tumor was surgically resected with no chemotherapy given. Now 9 years post resection she demonstrates no local or distant recurrence and stable renal function.
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spelling pubmed-54612662017-06-21 A Challenging Case of Hepatoblastoma Concomitant with Autosomal Recessive Polycystic Kidney Disease and Caroli Syndrome—Review of the Literature Kadakia, Nevil Lobritto, Steven J. Ovchinsky, Nadia Remotti, Helen E. Yamashiro, Darrell J. Emond, Jean C. Martinez, Mercedes Front Pediatr Pediatrics We report a rare case of an 18-month-old female with autosomal recessive polycystic kidney disease, Caroli syndrome, and pure fetal type hepatoblastoma. The liver tumor was surgically resected with no chemotherapy given. Now 9 years post resection she demonstrates no local or distant recurrence and stable renal function. Frontiers Media S.A. 2017-06-07 /pmc/articles/PMC5461266/ /pubmed/28638817 http://dx.doi.org/10.3389/fped.2017.00114 Text en Copyright © 2017 Kadakia, Lobritto, Ovchinsky, Remotti, Yamashiro, Emond and Martinez. http://creativecommons.org/licenses/by/4.0/ This is an open-access article distributed under the terms of the Creative Commons Attribution License (CC BY). The use, distribution or reproduction in other forums is permitted, provided the original author(s) or licensor are credited and that the original publication in this journal is cited, in accordance with accepted academic practice. No use, distribution or reproduction is permitted which does not comply with these terms.
spellingShingle Pediatrics
Kadakia, Nevil
Lobritto, Steven J.
Ovchinsky, Nadia
Remotti, Helen E.
Yamashiro, Darrell J.
Emond, Jean C.
Martinez, Mercedes
A Challenging Case of Hepatoblastoma Concomitant with Autosomal Recessive Polycystic Kidney Disease and Caroli Syndrome—Review of the Literature
title A Challenging Case of Hepatoblastoma Concomitant with Autosomal Recessive Polycystic Kidney Disease and Caroli Syndrome—Review of the Literature
title_full A Challenging Case of Hepatoblastoma Concomitant with Autosomal Recessive Polycystic Kidney Disease and Caroli Syndrome—Review of the Literature
title_fullStr A Challenging Case of Hepatoblastoma Concomitant with Autosomal Recessive Polycystic Kidney Disease and Caroli Syndrome—Review of the Literature
title_full_unstemmed A Challenging Case of Hepatoblastoma Concomitant with Autosomal Recessive Polycystic Kidney Disease and Caroli Syndrome—Review of the Literature
title_short A Challenging Case of Hepatoblastoma Concomitant with Autosomal Recessive Polycystic Kidney Disease and Caroli Syndrome—Review of the Literature
title_sort challenging case of hepatoblastoma concomitant with autosomal recessive polycystic kidney disease and caroli syndrome—review of the literature
topic Pediatrics
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5461266/
https://www.ncbi.nlm.nih.gov/pubmed/28638817
http://dx.doi.org/10.3389/fped.2017.00114
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