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The Role of the Heat Shock Protein B8 (HSPB8) in Motoneuron Diseases

Amyotrophic lateral sclerosis (ALS) and spinal and bulbar muscular atrophy (SBMA) are two motoneuron diseases (MNDs) characterized by aberrant protein behavior in affected cells. In familial ALS (fALS) and in SBMA specific gene mutations lead to the production of neurotoxic proteins or peptides pron...

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Detalles Bibliográficos
Autores principales:	Rusmini, Paola, Cristofani, Riccardo, Galbiati, Mariarita, Cicardi, Maria E., Meroni, Marco, Ferrari, Veronica, Vezzoli, Giulia, Tedesco, Barbara, Messi, Elio, Piccolella, Margherita, Carra, Serena, Crippa, Valeria, Poletti, Angelo
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Frontiers Media S.A. 2017
Materias:	Neuroscience
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5478700/ https://www.ncbi.nlm.nih.gov/pubmed/28680390 http://dx.doi.org/10.3389/fnmol.2017.00176

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