Cargando…

Severe dyspnea in a patient with neurofibromatosis type 1

Neurofibromatosis type 1 (NF1) is a genetic disease in which pulmonary complications are rare, but severe, especially pulmonary hypertension (PH). The mechanisms underlying the onset of PH in patients with NF1 are unclear and might be multifactorial. In particular, the frequent presence of pulmonary...

Descripción completa

Detalles Bibliográficos
Autores principales: Poble, P.B., Dalphin, J.C., Degano, B.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2017
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5491756/
https://www.ncbi.nlm.nih.gov/pubmed/28702341
http://dx.doi.org/10.1016/j.rmcr.2017.06.008