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Surgical correction of hyperlordosis in facioscapulohumeral muscular dystrophy: A case report

BACKGROUND: Hyperlordosis is common in facioscapulohumeral muscular dystrophy (FSHD), which cannot be controlled by bracing. While the surgical treatment is neither reported nor recommended in previous studies, we report the first corrective surgery for hyperlordosis in one wheelchair-dependent FSHD...

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Autores principales: Tan, Haining, Feng, Fan, Lin, Youxi, Chen, Chong, Li, Zheng, Shen, Jianxiong
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2017
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5513136/
https://www.ncbi.nlm.nih.gov/pubmed/28716073
http://dx.doi.org/10.1186/s12893-017-0276-0
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author Tan, Haining
Feng, Fan
Lin, Youxi
Chen, Chong
Li, Zheng
Shen, Jianxiong
author_facet Tan, Haining
Feng, Fan
Lin, Youxi
Chen, Chong
Li, Zheng
Shen, Jianxiong
author_sort Tan, Haining
collection PubMed
description BACKGROUND: Hyperlordosis is common in facioscapulohumeral muscular dystrophy (FSHD), which cannot be controlled by bracing. While the surgical treatment is neither reported nor recommended in previous studies, we report the first corrective surgery for hyperlordosis in one wheelchair-dependent FSHD patient. CASE PRESENTATION: A 15-year-old, wheelchair-dependent girl complaining of hyperlordosis and lower extremity weakness was diagnosed as FSHD. Preoperative examination showed hyperlordosis of 116° with scoliosis of 44°. Posterior correction and bone graft fusion was performed. Postoperatively, the hyperlordosis was corrected to 72° and better sitting posture was gotten. 12 months’ follow-up showed favorable correction with improvement in SF-36 and ODI score. CONCLUSIONS: The correction for hyperlordosis in FSHD is controversial. We report the first successful case of operative treatment by corrective spine surgery in these rare and demanding patient collective. Corrective surgery for spinal deformity, such as hyperlordosis and scoliosis, could do some help in posture and improve the quality of life especially in wheelchair-dependent patients.
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spelling pubmed-55131362017-07-19 Surgical correction of hyperlordosis in facioscapulohumeral muscular dystrophy: A case report Tan, Haining Feng, Fan Lin, Youxi Chen, Chong Li, Zheng Shen, Jianxiong BMC Surg Case Report BACKGROUND: Hyperlordosis is common in facioscapulohumeral muscular dystrophy (FSHD), which cannot be controlled by bracing. While the surgical treatment is neither reported nor recommended in previous studies, we report the first corrective surgery for hyperlordosis in one wheelchair-dependent FSHD patient. CASE PRESENTATION: A 15-year-old, wheelchair-dependent girl complaining of hyperlordosis and lower extremity weakness was diagnosed as FSHD. Preoperative examination showed hyperlordosis of 116° with scoliosis of 44°. Posterior correction and bone graft fusion was performed. Postoperatively, the hyperlordosis was corrected to 72° and better sitting posture was gotten. 12 months’ follow-up showed favorable correction with improvement in SF-36 and ODI score. CONCLUSIONS: The correction for hyperlordosis in FSHD is controversial. We report the first successful case of operative treatment by corrective spine surgery in these rare and demanding patient collective. Corrective surgery for spinal deformity, such as hyperlordosis and scoliosis, could do some help in posture and improve the quality of life especially in wheelchair-dependent patients. BioMed Central 2017-07-17 /pmc/articles/PMC5513136/ /pubmed/28716073 http://dx.doi.org/10.1186/s12893-017-0276-0 Text en © The Author(s). 2017 Open AccessThis article is distributed under the terms of the Creative Commons Attribution 4.0 International License (http://creativecommons.org/licenses/by/4.0/), which permits unrestricted use, distribution, and reproduction in any medium, provided you give appropriate credit to the original author(s) and the source, provide a link to the Creative Commons license, and indicate if changes were made. The Creative Commons Public Domain Dedication waiver (http://creativecommons.org/publicdomain/zero/1.0/) applies to the data made available in this article, unless otherwise stated.
spellingShingle Case Report
Tan, Haining
Feng, Fan
Lin, Youxi
Chen, Chong
Li, Zheng
Shen, Jianxiong
Surgical correction of hyperlordosis in facioscapulohumeral muscular dystrophy: A case report
title Surgical correction of hyperlordosis in facioscapulohumeral muscular dystrophy: A case report
title_full Surgical correction of hyperlordosis in facioscapulohumeral muscular dystrophy: A case report
title_fullStr Surgical correction of hyperlordosis in facioscapulohumeral muscular dystrophy: A case report
title_full_unstemmed Surgical correction of hyperlordosis in facioscapulohumeral muscular dystrophy: A case report
title_short Surgical correction of hyperlordosis in facioscapulohumeral muscular dystrophy: A case report
title_sort surgical correction of hyperlordosis in facioscapulohumeral muscular dystrophy: a case report
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5513136/
https://www.ncbi.nlm.nih.gov/pubmed/28716073
http://dx.doi.org/10.1186/s12893-017-0276-0
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