Cargando…

COLQ-mutant Congenital Myasthenic Syndrome with Microcephaly: A Unique Case with Literature Review

Congenital Myasthenic Syndrome (CMS) is a group of inherited neuromuscular junction disorders caused by defects in several genes. Clinical features include delayed motor milestones, recurrent respiratory illnesses and variable fatigable weakness. The central nervous system involvement is typically n...

Descripción completa

Detalles Bibliográficos
Autores principales: Al-Muhaizea, Mohammad A., Al-Mobarak, Sulaiman Bazee
Formato: Online Artículo Texto
Lenguaje:English
Publicado: De Gruyter Open 2017
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5518714/
https://www.ncbi.nlm.nih.gov/pubmed/28744372
http://dx.doi.org/10.1515/tnsci-2017-0011
_version_ 1783251529482895360
author Al-Muhaizea, Mohammad A.
Al-Mobarak, Sulaiman Bazee
author_facet Al-Muhaizea, Mohammad A.
Al-Mobarak, Sulaiman Bazee
author_sort Al-Muhaizea, Mohammad A.
collection PubMed
description Congenital Myasthenic Syndrome (CMS) is a group of inherited neuromuscular junction disorders caused by defects in several genes. Clinical features include delayed motor milestones, recurrent respiratory illnesses and variable fatigable weakness. The central nervous system involvement is typically not part of the CMS. We report here a Saudi girl with genetically proven Collagen Like Tail Subunit Of Asymmetric Acetylcholinesterase (COLQ) mutation type CMS who has global developmental delay, microcephaly and respiratory failure. We have reviewed the literature regarding COLQ-type CMS and to the best of our knowledge this is the first ever reported association of congenital myasthenia syndrome with microcephaly.
format Online
Article
Text
id pubmed-5518714
institution National Center for Biotechnology Information
language English
publishDate 2017
publisher De Gruyter Open
record_format MEDLINE/PubMed
spelling pubmed-55187142017-07-25 COLQ-mutant Congenital Myasthenic Syndrome with Microcephaly: A Unique Case with Literature Review Al-Muhaizea, Mohammad A. Al-Mobarak, Sulaiman Bazee Transl Neurosci Regular Articles Congenital Myasthenic Syndrome (CMS) is a group of inherited neuromuscular junction disorders caused by defects in several genes. Clinical features include delayed motor milestones, recurrent respiratory illnesses and variable fatigable weakness. The central nervous system involvement is typically not part of the CMS. We report here a Saudi girl with genetically proven Collagen Like Tail Subunit Of Asymmetric Acetylcholinesterase (COLQ) mutation type CMS who has global developmental delay, microcephaly and respiratory failure. We have reviewed the literature regarding COLQ-type CMS and to the best of our knowledge this is the first ever reported association of congenital myasthenia syndrome with microcephaly. De Gruyter Open 2017-07-20 /pmc/articles/PMC5518714/ /pubmed/28744372 http://dx.doi.org/10.1515/tnsci-2017-0011 Text en © 2017 Mohammad A. Al-Muhaizea, Sulaiman Bazee Al-Mobarak http://creativecommons.org/licenses/by-nc-nd/3.0 This work is licensed under the Creative Commons Attribution-NonCommercial-NoDerivatives 3.0 License.
spellingShingle Regular Articles
Al-Muhaizea, Mohammad A.
Al-Mobarak, Sulaiman Bazee
COLQ-mutant Congenital Myasthenic Syndrome with Microcephaly: A Unique Case with Literature Review
title COLQ-mutant Congenital Myasthenic Syndrome with Microcephaly: A Unique Case with Literature Review
title_full COLQ-mutant Congenital Myasthenic Syndrome with Microcephaly: A Unique Case with Literature Review
title_fullStr COLQ-mutant Congenital Myasthenic Syndrome with Microcephaly: A Unique Case with Literature Review
title_full_unstemmed COLQ-mutant Congenital Myasthenic Syndrome with Microcephaly: A Unique Case with Literature Review
title_short COLQ-mutant Congenital Myasthenic Syndrome with Microcephaly: A Unique Case with Literature Review
title_sort colq-mutant congenital myasthenic syndrome with microcephaly: a unique case with literature review
topic Regular Articles
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5518714/
https://www.ncbi.nlm.nih.gov/pubmed/28744372
http://dx.doi.org/10.1515/tnsci-2017-0011
work_keys_str_mv AT almuhaizeamohammada colqmutantcongenitalmyasthenicsyndromewithmicrocephalyauniquecasewithliteraturereview
AT almobaraksulaimanbazee colqmutantcongenitalmyasthenicsyndromewithmicrocephalyauniquecasewithliteraturereview