Two-Stage Urethroplasty with Buccal Mucosa for Penoscrotal Hypospadias Reconstruction in a Male with a 46,XX Karyotype

We present a case regarding a 32-year old African male with penoscrotal hypospadias, left cryptorchidism and a left inguinal hernia. There were moderate masculinization characteristics. He underwent a Lichtenstein hernia repair with perioperative biopsies of the left inguinal testis and epididymis....

Descripción completa

Detalles Bibliográficos
Autores principales: D'hulst, Pieter, Darras, Jochen, Joniau, Steven, Mattelaer, Pieter, Winne, Linsey, Ponette, Diederik
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2017
Materias:
Trauma and Reconstruction
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5522374/
https://www.ncbi.nlm.nih.gov/pubmed/28752067
http://dx.doi.org/10.1016/j.eucr.2017.06.016
Descripción
Sumario:We present a case regarding a 32-year old African male with penoscrotal hypospadias, left cryptorchidism and a left inguinal hernia. There were moderate masculinization characteristics. He underwent a Lichtenstein hernia repair with perioperative biopsies of the left inguinal testis and epididymis. Microscopic examination showed a Sertoli-only left testis with Leydig-cell hyperplasia and the left epididymis consisted of ovarian tissue with corpora albicantia and maturing follicles. Endocrinological evaluation showed a sex-determining region Y (SRY) negative 46,XX karyotype. We successfully performed a two-stage urethroplasty with buccal mucosa graft to reconstruct his penoscrotal hypospadias.

Ejemplares similares