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The Role of Sulfide Oxidation Impairment in the Pathogenesis of Primary CoQ Deficiency

Coenzyme Q (CoQ) is a lipid present in all cell membranes. One of the multiple metabolic functions of CoQ is to transport electrons in the reaction catalyzed by sulfide:quinone oxidoreductase (SQOR), the first enzyme of the oxidation pathway of sulfides (hydrogen sulfide, H(2)S). Early evidence of a...

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Detalles Bibliográficos
Autores principales:	Quinzii, Catarina M., Luna-Sanchez, Marta, Ziosi, Marcello, Hidalgo-Gutierrez, Agustin, Kleiner, Giulio, Lopez, Luis C.
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Frontiers Media S.A. 2017
Materias:	Physiology
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5525000/ https://www.ncbi.nlm.nih.gov/pubmed/28790927 http://dx.doi.org/10.3389/fphys.2017.00525

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