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Retroperitoneal fibrosis – a report of five cases
Retroperitoneal fibrosis (RPF) is a rare disease, characterized by inflammation and deposition of fibrotic tissue in the vicinity of the abdominal aorta and iliac arteries. We present a report of five patients admitted to our department between January 2014 and February 2017, diagnosed with RPF. Abd...
Autores principales: | , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Narodowy Instytut Geriatrii, Reumatologii i Rehabilitacji w Warszawie
2017
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5534509/ https://www.ncbi.nlm.nih.gov/pubmed/28769138 http://dx.doi.org/10.5114/reum.2017.68914 |
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author | Runowska, Marta Majewski, Dominik Puszczewicz, Mariusz |
author_facet | Runowska, Marta Majewski, Dominik Puszczewicz, Mariusz |
author_sort | Runowska, Marta |
collection | PubMed |
description | Retroperitoneal fibrosis (RPF) is a rare disease, characterized by inflammation and deposition of fibrotic tissue in the vicinity of the abdominal aorta and iliac arteries. We present a report of five patients admitted to our department between January 2014 and February 2017, diagnosed with RPF. Abdominal pain was the most common presenting symptom; however, in one patient, RPF was identified accidentally in routinely performed ultrasonography. In 4 cases, corticosteroids (CS) in combination with azathioprine were applied as first-line therapy, whereas one patient was treated with intravenous methylprednisolone pulses followed by oral CS. In this paper, clinical features as well as laboratory and radiographic findings together with management and treatment outcomes in patients with RPF are discussed. Given the rarity of the condition, it seems important to report every single case of RPF to help establish its management algorithm. |
format | Online Article Text |
id | pubmed-5534509 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2017 |
publisher | Narodowy Instytut Geriatrii, Reumatologii i Rehabilitacji w Warszawie |
record_format | MEDLINE/PubMed |
spelling | pubmed-55345092017-08-02 Retroperitoneal fibrosis – a report of five cases Runowska, Marta Majewski, Dominik Puszczewicz, Mariusz Reumatologia Case Report Retroperitoneal fibrosis (RPF) is a rare disease, characterized by inflammation and deposition of fibrotic tissue in the vicinity of the abdominal aorta and iliac arteries. We present a report of five patients admitted to our department between January 2014 and February 2017, diagnosed with RPF. Abdominal pain was the most common presenting symptom; however, in one patient, RPF was identified accidentally in routinely performed ultrasonography. In 4 cases, corticosteroids (CS) in combination with azathioprine were applied as first-line therapy, whereas one patient was treated with intravenous methylprednisolone pulses followed by oral CS. In this paper, clinical features as well as laboratory and radiographic findings together with management and treatment outcomes in patients with RPF are discussed. Given the rarity of the condition, it seems important to report every single case of RPF to help establish its management algorithm. Narodowy Instytut Geriatrii, Reumatologii i Rehabilitacji w Warszawie 2017-07-18 2017 /pmc/articles/PMC5534509/ /pubmed/28769138 http://dx.doi.org/10.5114/reum.2017.68914 Text en Copyright: © 2017 Narodowy Instytut Geriatrii, Reumatologii i Rehabilitacji w Warszawie http://creativecommons.org/licenses/by-nc-sa/4.0/ This is an Open Access article distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 International (CC BY-NC-SA 4.0) License, allowing third parties to copy and redistribute the material in any medium or format and to remix, transform, and build upon the material, provided the original work is properly cited and states its license. |
spellingShingle | Case Report Runowska, Marta Majewski, Dominik Puszczewicz, Mariusz Retroperitoneal fibrosis – a report of five cases |
title | Retroperitoneal fibrosis – a report of five cases |
title_full | Retroperitoneal fibrosis – a report of five cases |
title_fullStr | Retroperitoneal fibrosis – a report of five cases |
title_full_unstemmed | Retroperitoneal fibrosis – a report of five cases |
title_short | Retroperitoneal fibrosis – a report of five cases |
title_sort | retroperitoneal fibrosis – a report of five cases |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5534509/ https://www.ncbi.nlm.nih.gov/pubmed/28769138 http://dx.doi.org/10.5114/reum.2017.68914 |
work_keys_str_mv | AT runowskamarta retroperitonealfibrosisareportoffivecases AT majewskidominik retroperitonealfibrosisareportoffivecases AT puszczewiczmariusz retroperitonealfibrosisareportoffivecases |