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Is Asphyxiating Thoracic Dystrophy (Jeune's Syndrome) Deadly and Should We Insist on Treating It? Reconstructive Surgery “On Demand”
Our aim is to present the treatment of one of the skeletal manifestations of Jeune's syndrome (JS), the hypoplastic chest, which can result in thoracic insufficiency syndrome and present “on-demand” stage surgical technique using mandible locking plate system for the fixation of ribs. The diagn...
Autores principales: | Drebov, Rosen Stanchev, Katsarov, Atanas, Gagov, Emiliyan, Atanasova, Nia, Penev, Zlatin, Iliev, Alexander |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Thieme Medical Publishers
2017
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Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5553486/ https://www.ncbi.nlm.nih.gov/pubmed/28825014 http://dx.doi.org/10.1055/s-0037-1598043 |
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